Protein folding alterations in amyotrophic lateral sclerosis

Brain Research

Volumn 1648, Issue , 2016, Pages 633-649

  Parakh, Sonam ^a   Atkin, Julie D ^a,b  

^a MACQUARIE UNIVERSITY   (Australia)

^b LA TROBE UNIVERSITY   (Australia)

Author keywords

Amyotrophic lateral sclerosis; C9ORF72; Disulphide bonds; ER stress; FUS; Protein disulphide isomerase (PDI); Protein misfolding; Superoxide dismutase 1 (SOD1); TDP 43

Indexed keywords

CELL PROTEIN; CHAPERONE; COPPER ZINC SUPEROXIDE DISMUTASE; FUSED IN SARCOMA PROTEIN; PROTEASOME; PROTEIN CHROMOSOME 9 OPEN READING FRAME 72; TAR DNA BINDING PROTEIN; UBIQUITIN; UNCLASSIFIED DRUG; DNA BINDING PROTEIN; FUS PROTEIN, HUMAN; GUANINE NUCLEOTIDE EXCHANGE C9ORF72; RNA BINDING PROTEIN FUS; SOD1 PROTEIN, HUMAN; TDP-43 PROTEIN, HUMAN;

AMYOTROPHIC LATERAL SCLEROSIS; AUTOPHAGY; BRAIN STEM; CELL BODY; CELL MIGRATION; CHROMOSOME 9; DEGENERATIVE DISEASE; DISULFIDE BOND; ENDOPLASMIC RETICULUM; ENDOPLASMIC RETICULUM STRESS; GOLGI COMPLEX; HUMAN; MOTONEURON; NERVE FIBER TRANSPORT; NONHUMAN; OPEN READING FRAME; OXIDATIVE STRESS; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN DEGRADATION; PROTEIN FOLDING; PROTEIN FUNCTION; PROTEIN MISFOLDING; PROTEIN TARGETING; REVIEW; SPINAL CORD; ANIMAL; GENETICS; METABOLISM; MUTATION; PATHOPHYSIOLOGY; PROTEOSTASIS DEFICIENCY;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; C9ORF72 PROTEIN; DNA-BINDING PROTEINS; HUMANS; MOLECULAR CHAPERONES; MUTATION; PROTEIN FOLDING; PROTEOSTASIS DEFICIENCIES; RNA-BINDING PROTEIN FUS; SUPEROXIDE DISMUTASE-1;

EID: 84975746049     PISSN: 00068993     EISSN: 18726240     Source Type: Journal    
DOI: 10.1016/j.brainres.2016.04.010     Document Type: Review

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