Disulfide cross-linked protein represents a significant fraction of ALS-associated Cu, Zn-superoxide dismutase aggregates in spinal cords of model mice

Proceedings of the National Academy of Sciences of the United States of America

Volumn 103, Issue 18, 2006, Pages 7148-7153

  Furukawa, Yoshiaki ^a   Fu, Ronggen ^b   Deng, Han Xiang ^b   Siddique, Teepu ^b   O'Halloran, Thomas V ^a  

^a NORTHWESTERN UNIVERSITY   (United States)

^b NORTHWESTERN UNIVERSITY   (United States)

Author keywords

Disulfide bond; Neurodegnerative disease; Oxidative stress; Protein aggregation

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; MUTANT PROTEIN;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN CORTEX; CONTROLLED STUDY; CROSS LINKING; DEGENERATIVE DISEASE; DISULFIDE BOND; FAMILIAL DISEASE; HISTOPATHOLOGY; IN VITRO STUDY; LIVER; MOTONEURON; MOUSE; NERVE CELL NECROSIS; NONHUMAN; OLIGOMERIZATION; OXIDATIVE STRESS; POINT MUTATION; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN FOLDING; PROTEIN STABILITY; SPINAL CORD; SYMPTOMATOLOGY; TRANSGENIC MOUSE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CROSS-LINKING REAGENTS; CYSTEINE; DISULFIDES; HUMANS; MICE; MICE, TRANSGENIC; MODELS, MOLECULAR; OXIDATION-REDUCTION; OXIDATIVE STRESS; PROTEIN CONFORMATION; PROTEIN FOLDING; SPINAL CORD; SUPEROXIDE DISMUTASE;

ANIMALIA; MUS MUSCULUS;

EID: 33646486372     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.0602048103     Document Type: Article

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