The wobbler mouse, an ALS animal model

Molecular Genetics and Genomics

Volumn 288, Issue 5-6, 2013, Pages 207-229

  Moser, Jakob Maximilian ^a   Bigini, Paolo ^b   Schmitt John, Thomas ^a  

^a AARHUS UNIVERSITY   (Denmark)

^b MARIO NEGRI INSTITUTE FOR PHARMACOLOGICAL RESEARCH   (Italy)

Author keywords

ALS; GARP complex; Motor neuron degeneration; Vesicle tethering; Wobbler

Indexed keywords

21 [4 [2,6 BIS(1 PYRROLIDINYL) 4 PYRIMIDINYL] 1 PIPERAZINYL]PREGNA 1,4,9(11) TRIENE 3,20 DIONE; ANTIINFLAMMATORY AGENT; ANTIOXIDANT; BRAIN DERIVED NEUROTROPHIC FACTOR; CARDIOTROPHIN 1; CILIARY NEUROTROPHIC FACTOR; CREATININE MONOHYDRATE; ERYTHROPOIETIN; GARP COMPLEX; INTERLEUKIN 6; INTERLEUKIN 6 RECEPTOR; LECITHINIZED SUPEROXIDE DISMUTASE; LEUKEMIA INHIBITORY FACTOR; MULTIPROTEIN COMPLEX; N (7 HYDROXY 2,2,4,6 TETRAMETHYL 1 INDANYL) 4 (3 METHOXYPHENYL) 1 PIPERAZINEACETAMIDE; N(G) NITROARGININE METHYL ESTER; PROGESTERONE; RECOMBINANT INSULIN LIKE GROWTH FACTOR; RILUZOLE; SOLUBLE INTERLEUKIN 6 RECEPTOR; SOMATOMEDIN; TUMOR NECROSIS FACTOR BINDING PROTEIN 1; U 74389 F; UNCLASSIFIED DRUG; VB 3323;

AMNIOTIC FLUID CELL THERAPY; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; CELL THERAPY; CORD BLOOD MONONUCLEAR CELL THERAPY; DISEASE COURSE; DISEASE MODEL; DRUG MECHANISM; GENE; GENE LOCUS; GENE MUTATION; GENETIC IDENTIFICATION; HUMAN; HYPERBARIC OXYGEN; MOLECULAR PATHOLOGY; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; SKELETAL MUSCLE DERIVED STEM CELL THERAPY; SPERMATOGENESIS; STEM CELL TRANSPLANTATION; VPS54 GENE; WOBBLER MOUSE;

AMINO ACID SEQUENCE; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; ANTI-INFLAMMATORY AGENTS; ANTIOXIDANTS; DISEASE MODELS, ANIMAL; HUMANS; MALE; MICE; MOLECULAR SEQUENCE DATA; MOTOR NEURON DISEASE; MUTATION; SPERMATOGENESIS; VESICULAR TRANSPORT PROTEINS;

ANIMALIA;

EID: 84878765869     PISSN: 16174615     EISSN: 16174623     Source Type: Journal    
DOI: 10.1007/s00438-013-0741-0     Document Type: Article

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