Mutant SOD1 inhibits ER-Golgi transport in amyotrophic lateral sclerosis

Journal of Neurochemistry

Volumn 129, Issue 1, 2014, Pages 190-204

  Atkin, Julie D ^a,b   Farg, Manal A ^a   Soo, Kai Ying ^a   Walker, Adam K ^a,e   Halloran, Mark ^a   Turner, Bradley J ^b   Nagley, Phillip ^c   Horne, Malcolm K ^b,d  

^a LA TROBE UNIVERSITY   (Australia)

^b UNIVERSITY OF MELBOURNE   (Australia)

^c MONASH UNIVERSITY   (Australia)

^d ST VINCENT S HOSPITAL   (Australia)

^e UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

amyotrophic lateral sclerosis; ER Golgi transport; neurodegeneration

Indexed keywords

COAT PROTEIN; COPPER ZINC SUPEROXIDE DISMUTASE; MUTANT PROTEIN; PROTEIN SAR1; SECRETORY PROTEIN; UNCLASSIFIED DRUG;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; CELL DAMAGE; CONTROLLED STUDY; CYTOPLASM; DISEASE ACTIVITY; ENDOPLASMIC RETICULUM; ENDOPLASMIC RETICULUM STRESS; ENZYME ACTIVITY; ENZYME LOCALIZATION; FEMALE; GOLGI COMPLEX; INTRACELLULAR TRANSPORT; MOUSE; NERVE CELL; NERVE FIBER TRANSPORT; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN EXPRESSION; PROTEIN PROTEIN INTERACTION; PROTEIN TRANSPORT;

AMYOTROPHIC LATERAL SCLEROSIS; ER-GOLGI TRANSPORT; NEURODEGENERATION;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CHO CELLS; CRICETINAE; CRICETULUS; ENDOPLASMIC RETICULUM; FEMALE; GOLGI APPARATUS; HUMANS; MICE; MICE, TRANSGENIC; MUTATION; PROTEIN TRANSPORT; SUPEROXIDE DISMUTASE;

EID: 84897112194     PISSN: 00223042     EISSN: 14714159     Source Type: Journal    
DOI: 10.1111/jnc.12493     Document Type: Article

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