Potential effect of S-nitrosylated protein disulfide isomerase on mutant SOD1 aggregation and neuronal cell death in amyotrophic lateral sclerosis

Molecular Neurobiology

Volumn 49, Issue 2, 2014, Pages 796-807

  Jeon, Gye Sun ^a   Nakamura, Tomohiro ^b   Lee, Jeong Seon ^a   Choi, Won Jun ^c   Ahn, Suk Won ^d   Lee, Kwang Woo ^a   Sung, Jung Joon ^a   Lipton, Stuart A ^b  

^a Seoul National University Hospital   (South Korea)

^b BURNHAM INSTITUTE   (United States)

^c Hanyang University College of Medicine   (South Korea)

^d Chung Ang University College of Medicine   (South Korea)

Author keywords

ALS; ER stress; Protein disulfide isomerase; S nitrosylation; SOD1

Indexed keywords

BIOTIN; COPPER ZINC SUPEROXIDE DISMUTASE; PROTEIN DISULFIDE ISOMERASE; THAPSIGARGIN; SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ARTICLE; CONTROLLED STUDY; ENDOPLASMIC RETICULUM STRESS; HUMAN; HUMAN CELL; NERVE CELL NECROSIS; NEUROTOXICITY; NITROSYLATION; NONHUMAN; PROTEIN AGGREGATION; RAT; ANIMAL; BIOSYNTHESIS; CELL DEATH; ENZYMOLOGY; FEMALE; GENETICS; HEK293 CELL LINE; METABOLISM; MOUSE; MUTATION; NERVE CELL; PATHOLOGY; PHYSIOLOGY; TRANSGENIC MOUSE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CELL DEATH; FEMALE; HEK293 CELLS; HUMANS; MICE; MICE, TRANSGENIC; MUTATION; NEURONS; PROTEIN DISULFIDE-ISOMERASES; SUPEROXIDE DISMUTASE;

EID: 84896498656     PISSN: 08937648     EISSN: 15591182     Source Type: Journal    
DOI: 10.1007/s12035-013-8562-z     Document Type: Article

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