Extracellular wildtype and mutant SOD1 induces ER-Golgi pathology characteristic of amyotrophic lateral sclerosis in neuronal cells

Cellular and Molecular Life Sciences

Volumn 70, Issue 21, 2013, Pages 4181-4195

  Sundaramoorthy, Vinod ^a   Walker, Adam K ^a,b   Yerbury, Justin ^c   Soo, Kai Ying ^a   Farg, Manal A ^a   Hoang, Vy ^a   Zeineddine, Rafaa ^c   Spencer, Damian ^a   Atkin, Julie D ^a,d  

^a LA TROBE UNIVERSITY   (Australia)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

^c UNIVERSITY OF WOLLONGONG   (Australia)

^d UNIVERSITY OF MELBOURNE   (Australia)

Author keywords

ALS; Endoplasmic reticulum; Extracellular; Golgi; SOD1

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; APOPTOSIS; ARTICLE; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; ENDOPLASMIC RETICULUM STRESS; GENE MUTATION; GOLGI COMPLEX; HUMAN; HUMAN CELL; INHIBITION KINETICS; MOTONEURON; MOUSE; NERVE CELL; NONHUMAN; PATHOGENESIS; PINOCYTOSIS; PROTEIN AGGREGATION; PROTEIN MISFOLDING; PROTEIN PURIFICATION; PROTEIN STRUCTURE; PROTEIN TRANSPORT; SOD1 GENE; WILD TYPE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; APOPTOSIS; CELL DEATH; CELL LINE; ENDOPLASMIC RETICULUM; GOLGI APPARATUS; HUMANS; IMMUNOHISTOCHEMISTRY; MICE; MOTOR NEURONS; MUTATION; NEURONS; PROTEIN FOLDING; SUPEROXIDE DISMUTASE;

EID: 84887069357     PISSN: 1420682X     EISSN: 14209071     Source Type: Journal    
DOI: 10.1007/s00018-013-1385-2     Document Type: Article

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