Decreased glutathione accelerates neurologiCal deficit and mitochondrial pathology in familial ALS-linked hSOD1G93A mice model

Neurobiology of Disease

Volumn 43, Issue 3, 2011, Pages 543-551

  Vargas, Marcelo R ^a   Johnson, Delinda A ^a   Johnson, Jeffrey A ^a,b  

^a UNIVERSITY OF WISCONSIN MADISON   (United States)

^b UNIVERSITY OF WISCONSIN MADISON   (United States)

Author keywords

Amyotrophic lateral sclerosis; GCLM; Glutathione; Mitochondria

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; GLUTAMATE CYSTEINE LIGASE; GLUTATHIONE;

AMINO ACID DEFICIENCY; AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL LOSS; CONTROLLED STUDY; FAMILIAL DISEASE; FERTILITY; GENE MUTATION; KNOCKOUT MOUSE; LIFESPAN; MATING; MITOCHONDRION; MOTONEURON; MOUSE; MOUSE MUTANT; NEUROLOGIC DISEASE; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN EXPRESSION; SURVIVAL;

ALANINE; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CELLS, CULTURED; COCULTURE TECHNIQUES; DISEASE MODELS, ANIMAL; FEMALE; GLUTATHIONE; GLYCINE; MALE; MICE; MICE, INBRED C3H; MICE, INBRED C57BL; MICE, KNOCKOUT; MICE, TRANSGENIC; MITOCHONDRIA; MOTOR NEURONS; SUPEROXIDE DISMUTASE;

EID: 79960276613     PISSN: 09699961     EISSN: 1095953X     Source Type: Journal    
DOI: 10.1016/j.nbd.2011.04.025     Document Type: Article

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