Neurotoxic protein oligomerisation associated with polyglutamine diseases

Acta Neuropathologica

Volumn 120, Issue 4, 2010, Pages 419-437

  Hands, Sarah L ^a   Wyttenbach, Andreas ^a  

^a UNIVERSITY OF SOUTHAMPTON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

CELL PROTEIN; POLYGLUTAMINE; REACTIVE OXYGEN METABOLITE;

CELL FUNCTION; CELLULAR DISTRIBUTION; CONFORMATIONAL TRANSITION; CYTOTOXICITY; DNA FLANKING REGION; GAIN OF FUNCTION MUTATION; GENE MUTATION; GENETIC TRANSCRIPTION; HUMAN; LOSS OF FUNCTION MUTATION; MEMBRANE DAMAGE; NEUROTOXICITY; NONHUMAN; OLIGOMERIZATION; POLYGLUTAMINE DISEASE; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN CLEAVAGE; PROTEIN DEFECT; PROTEIN METABOLISM; PROTEIN PROCESSING; PROTEIN STRUCTURE; REVIEW;

ANIMALS; CENTRAL NERVOUS SYSTEM DISEASES; HUMANS; MODELS, BIOLOGICAL; MUTATION; NERVE TISSUE PROTEINS; PEPTIDES; PROTEIN BINDING; PROTEIN CONFORMATION; PROTEIN FOLDING;

EID: 77956184558     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-010-0703-0     Document Type: Review

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