Expanded polyglutamine in the machado-joseph disease protein induces cell death in vitro and in vivo

Nature Genetics

Volumn 13, Issue 2, 1996, Pages 196-202

  Ikeda, Hanako ^a   Yamaguchi, Masahiro ^a   Sugai, Satoshi ^b   Aze, Yoshiya ^b   Narumiya, Shuh ^a   Kakizuka, Akira ^a  

^a KYOTO UNIVERSITY FACULTY OF MEDICINE   (Japan)

^b Ono Pharmaceutical   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

POLYGLUTAMIC ACID;

ANIMAL CELL; APOPTOSIS; ARTICLE; CELL DEATH; MACHADO JOSEPH DISEASE; NERVE DEGENERATION; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PURKINJE CELL;

ANIMALS; ANIMALS, NEWBORN; APOPTOSIS; BLOTTING, WESTERN; CELLS, CULTURED; CEREBELLUM; GENE DOSAGE; HAPLORHINI; HUMANS; IMMUNOHISTOCHEMISTRY; KIDNEY; MACHADO-JOSEPH DISEASE; MICE; MICE, TRANSGENIC; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PEPTIDE BIOSYNTHESIS; PEPTIDES; PRECIPITATION; PROTEIN BIOSYNTHESIS; PROTEINS; PURKINJE CELLS; RECOMBINANT PROTEINS; REPRESSOR PROTEINS; TRANSCRIPTION FACTORS; TRANSFECTION; TRINUCLEOTIDE REPEATS;

ANIMALIA; MUS MUSCULUS;

EID: 0030058208     PISSN: 10614036     EISSN: 15461718     Source Type: Journal    
DOI: 10.1038/ng0696-196     Document Type: Article

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