Axonal transport of N-terminal huntingtin suggests early pathology of corticostriatal projections in huntington disease

Journal of Neuropathology and Experimental Neurology

Volumn 58, Issue 2, 1999, Pages 165-173

  Sapp, Ellen ^a   Penney, John ^a   Young, Anne ^a   Aronin, Neil ^b   Vonsattel, Jean Paul ^a   DiFiglia, Marian ^a  

^a MASSACHUSETTS GENERAL HOSPITAL   (United States)

^b UNIVERSITY OF MASSACHUSETTS MEDICAL SCHOOL   (United States)

Author keywords

Cortex; Human brain; Huntingtin; Immunohistochemistry; Striatum

Indexed keywords

HUNTINGTIN; MUTANT PROTEIN;

ADULT; AGED; AMINO TERMINAL SEQUENCE; ARTICLE; BRAIN CORTEX; CAPSULA INTERNA; CAUDATE NUCLEUS; CELL INCLUSION; CLINICAL ARTICLE; CONTROLLED STUDY; CORPUS STRIATUM; DISEASE SEVERITY; DYSTROPHY; FRONTAL CORTEX; GLOBUS PALLIDUS; HUMAN; HUMAN TISSUE; HUNTINGTON CHOREA; NERVE CELL NECROSIS; NERVE FIBER TRANSPORT; NEURITE; NEUROPATHOLOGY; NEUROPIL; PRIORITY JOURNAL; PUTAMEN; WHITE MATTER;

EID: 0032987513     PISSN: 00223069     EISSN: None     Source Type: Journal    
DOI: 10.1097/00005072-199902000-00006     Document Type: Article

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