Post-translational modifications and protein quality control in motor neuron and polyglutamine diseases

Frontiers in Molecular Neuroscience

Volumn 10, Issue , 2017, Pages

  Sambataro, Fabio ^a   Pennuto, Maria ^b  

^a UNIVERSITY OF UDINE   (Italy)

^b UNIVERSITY OF TRENTO   (Italy)

Author keywords

Aggregation; Motor neuron disease; Polyglutamine disease; Post translational modifications; Protein degradation

Indexed keywords

ACTIVATING TRANSCRIPTION FACTOR 4; ANDROGEN RECEPTOR; ARGININE; ATAXIN 1; ATAXIN 2; ATAXIN 3; ATAXIN 7; CASEIN KINASE II; COPPER ZINC SUPEROXIDE DISMUTASE; CYCLIN DEPENDENT KINASE 5; GLYCOGEN SYNTHASE KINASE 3; GLYCOGEN SYNTHASE KINASE 3BETA; I KAPPA B KINASE; PARKIN; POLYGLUTAMINE; SIRTUIN 1; TAR DNA BINDING PROTEIN; VALOSIN CONTAINING PROTEIN;

ACETYLATION; AMYOTROPHIC LATERAL SCLEROSIS; DEGENERATIVE DISEASE; DENTATORUBROPALLIDOLUYSIAN ATROPHY; HUMAN; HUNTINGTON CHOREA; KENNEDY DISEASE; MOTOR NEURON DISEASE; NERVE DEGENERATION; NEUROTOXICITY; NONHUMAN; PALMITOYLATION; POLYGLUTAMINE DISEASE; PROTEIN AGGREGATION; PROTEIN DEGRADATION; PROTEIN METHYLATION; PROTEIN PHOSPHORYLATION; PROTEIN PROCESSING; PROTEIN QUALITY; REVIEW; SUMOYLATION; TDP 43 PROTEINOPATHY; UBIQUITINATION;

EID: 85018909265     PISSN: 16625099     EISSN: None     Source Type: Journal    
DOI: 10.3389/fnmol.2017.00082     Document Type: Review

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