Proteases acting on mutant huntingtin generate cleaved products that differentially build up cytoplasmic and nuclear inclusions

Molecular Cell

Volumn 10, Issue 2, 2002, Pages 259-269

  Lunkes, Astrid ^a   Lindenberg, Katrin S ^b   Ben Haem, Léa ^a   Weber, Chantal ^a   Devys, Didier ^a   Landwehrmeyer, G Bernhard ^b   Mandel, Jean Louis ^a   Trottier, Yvon ^a  

^a INSTITUT DE GÉNÉTIQUE ET DE BIOLOGIE MOLÉCULAIRE ET CELLULAIRE   (France)

^b UNIVERSITY OF ULM   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; ASPARTIC PROTEINASE; HUNTINGTIN; MUTANT PROTEIN; PROTEASOME;

AMINO ACID SEQUENCE; ANIMAL CELL; ANIMAL MODEL; ARTICLE; BRAIN; CELL INCLUSION; CELL LINE; CELL NUCLEUS; CELL NUCLEUS INCLUSION BODY; CONTROLLED STUDY; DISEASE MODEL; ENZYMATIC DEGRADATION; HUMAN; HUMAN TISSUE; HUNTINGTON CHOREA; NONHUMAN; PROTEIN DEGRADATION; PROTEIN DOMAIN; PROTEIN SECRETION;

ANIMALIA;

EID: 0036671821     PISSN: 10972765     EISSN: None     Source Type: Journal    
DOI: 10.1016/S1097-2765(02)00602-0     Document Type: Article

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