Ubiquitin-mediated sequestration of normal cellular proteins into polyglutamine aggregates

Proceedings of the National Academy of Sciences of the United States of America

Volumn 100, Issue 15, 2003, Pages 8892-8897

  Donaldson, Kathryn M ^a   Li, Wei ^a   Ching, Keith A ^a   Batalov, Serge ^a   Tsai, Chih Cheng ^b,c   Joazeiro, Claudio A P ^a  

^a GENOMICS INSTITUTE OF THE NOVARTIS RESEARCH FOUNDATION   (United States)

^b SALK INSTITUTE FOR BIOLOGICAL STUDIES   (United States)

^c RUTGERS ROBERT WOOD JOHNSON MEDICAL SCHOOL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ATAXIN 3; BINDING PROTEIN; CELL PROTEIN; POLYGLUTAMINE; PROTEASOME; PROTEIN P62; SEQUESTOSOME 1; UBIQUITIN; UBIQUITIN BINDING PROTEIN; UNCLASSIFIED DRUG;

AMINO ACID SEQUENCE; ARTICLE; BIOINFORMATICS; CONTROLLED STUDY; DEGENERATIVE DISEASE; HUMAN; HUMAN CELL; HUMAN GENOME; NUCLEOTIDE SEQUENCE; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN LOCALIZATION; PROTEIN MOTIF; PROTEIN PROCESSING; SPINOCEREBELLAR DEGENERATION;

AMINO ACID MOTIFS; AMINO ACID SEQUENCE; ANIMALS; BINDING SITES; CARRIER PROTEINS; CELL LINE; CYSTEINE ENDOPEPTIDASES; HUMANS; IMMEDIATE-EARLY PROTEINS; MOLECULAR SEQUENCE DATA; MULTIENZYME COMPLEXES; MUTATION; NERVE TISSUE PROTEINS; NEURODEGENERATIVE DISEASES; NUCLEAR PROTEINS; PEPTIDES; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEINS; RECOMBINANT FUSION PROTEINS; REPRESSOR PROTEINS; SEQUENCE HOMOLOGY, AMINO ACID; TRANSFECTION; UBIQUITIN;

ATAXIA;

EID: 0042808497     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.1530212100     Document Type: Article

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