Iron-sulfur cluster synthesis, iron homeostasis and oxidative stress in Friedreich ataxia

Molecular and Cellular Neuroscience

Volumn 55, Issue , 2013, Pages 50-61

  Vaubel, Rachael A ^a   Isaya, Grazia ^a  

^a MAYO CLINIC   (United States)

Author keywords

Anti oxidants; Frataxin; Friedreich ataxia; Heme; Iron chelators; Iron sulfur clusters; Mitochondria; Oxidative stress

Indexed keywords

FRATAXIN; HEME; IRON; IRON SULFUR CLUSTER; SULFUR; UNCLASSIFIED DRUG;

ARTICLE; FRIEDREICH ATAXIA; MITOCHONDRION; NONHUMAN; OXIDATION REDUCTION POTENTIAL; OXIDATIVE STRESS; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN FUNCTION; PROTEIN PROTEIN INTERACTION; SACCHAROMYCES CEREVISIAE; SYNTHESIS;

ANIMALS; FRIEDREICH ATAXIA; HOMEOSTASIS; HUMANS; IRON; IRON-BINDING PROTEINS; IRON-SULFUR PROTEINS; MITOCHONDRIA; OXIDATIVE STRESS;

EID: 84875582275     PISSN: 10447431     EISSN: 10959327     Source Type: Journal    
DOI: 10.1016/j.mcn.2012.08.003     Document Type: Article

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