Mitochondrial ferritin limits oxidative damage regulating mitochondrial iron availability: Hypothesis for a protective role in Friedreich ataxia

Human Molecular Genetics

Volumn 18, Issue 1, 2009, Pages 1-11

  Campanella, Alessandro ^a,b   Rovelli, Elisabetta ^c   Santambrogio, Paolo ^c   Cozzi, Anna ^c   Taroni, Franco ^d   Levi, Sonia ^b,c  

^a Research Unit of Molecular Neuroscience   (Italy)

^b VITA SALUTE SAN RAFFAELE UNIVERSITY   (Italy)

^c SAN RAFFAELE HOSPITAL   (Italy)

^d DEPARTMENT OF NEUROSURGERY   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE 5'TRIPHOSPHATE; ANTIMYCIN A1; CYTOSOL RECEPTOR; FRATAXIN; GLUCOSE; IRON; MITOCHONDRIAL FERRITIN; MITOCHONDRIAL PROTEIN; PHOSPHATE; REACTIVE OXYGEN METABOLITE; UNCLASSIFIED DRUG; WATER;

ANIMAL TISSUE; ARTICLE; BRAIN MITOCHONDRION; CELL GROWTH; CELL PROTECTION; CELL VIABILITY; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME REGULATION; FIBROBLAST; FRIEDREICH ATAXIA; HOMEOSTASIS AND REGULATION; HUMAN; HUMAN CELL; MITOCHONDRIAL RESPIRATION; MOUSE; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN FUNCTION;

ANIMALS; CELLS, CULTURED; FERRITINS; FIBROBLASTS; FRIEDREICH ATAXIA; GENE EXPRESSION; GENE EXPRESSION REGULATION; HELA CELLS; HUMANS; IRON; MICE; MITOCHONDRIA; MITOCHONDRIAL PROTEINS; OXIDATION-REDUCTION; OXIDATIVE STRESS; REACTIVE OXYGEN SPECIES;

MAMMALIA; MUS;

EID: 57649243073     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddn308     Document Type: Article

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