Actin Glutathionylation Increases in Fibroblasts of Patients with Friedreich's Ataxia: A potential role in the pathogenesis of the disease

Journal of Biological Chemistry

Volumn 278, Issue 43, 2003, Pages 42588-42595

  Pastore, Anna ^a   Tozzi, Giulia ^a   Gaeta, Laura Maria ^a   Bertini, Enrico ^a   Serafini, Valentina ^a   Di Cesare, Silvia ^a   Bonetto, Valentina ^b   Casoni, Filippo ^b   Carrozzo, Rosalba ^a   Federici, Giorgio ^a   Piemonte, Fiorella ^a  

^a BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

^b MARIO NEGRI INSTITUTE FOR PHARMACOLOGICAL RESEARCH   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

HIGH PRESSURE LIQUID CHROMATOGRAPHY; IRON; METABOLISM; OXIDATION; PROTEINS; REDOX REACTIONS;

FIBROBLASTS;

DRUG PRODUCTS;

ACTIN; EOSIN; F ACTIN; FERROUS SULFATE; FRATAXIN; GLUTATHIONE; HEMATOXYLIN; IRON; PHALLOIDIN; REACTIVE OXYGEN METABOLITE; RHODAMINE;

ARTICLE; AUTOSOMAL RECESSIVE DISORDER; CELL FUNCTION; CELL VIABILITY; CHEMICAL REACTION; CONTROLLED STUDY; CYTOSKELETON; FEMALE; FIBROBLAST; FLUORESCENCE; FRIEDREICH ATAXIA; GLUTATHIONYLATION; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HUMAN; HUMAN CELL; IRON OVERLOAD; MALE; MICROFILAMENT; NERVE DEGENERATION; OXIDATION REDUCTION REACTION; OXIDATIVE STRESS; PATHOGENESIS; PRIORITY JOURNAL; STAINING; WESTERN BLOTTING;

ACTINS; ANTIOXIDANTS; BLOTTING, WESTERN; CASE-CONTROL STUDIES; CELLS, CULTURED; CHROMATOGRAPHY, HIGH PRESSURE LIQUID; FEMALE; FERROUS COMPOUNDS; FIBROBLASTS; FRIEDREICH ATAXIA; GLUTATHIONE; HUMANS; MALE; OXIDATION-REDUCTION; SKIN;

ATAXIA;

EID: 0142211205     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M301872200     Document Type: Article

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