Inactivation of the Friedreich ataxia mouse gene leads to early embryonic lethality without iron accumulation

Human Molecular Genetics

Volumn 9, Issue 8, 2000, Pages 1219-1226

  Cossée, Mireille ^a   Puccio, Hélène ^a   Gansmuller, Anne ^a   Koutnikova, Hana ^a   Dierich, Andrée ^a   LeMeur, Marianne ^a   Fischbeck, Kenneth ^a,b   Dollé, Pascal ^a   Kœnig, Michel ^a  

^a UNIVERSITY HOSPITAL OF STRASBOURG   (France)

^b NATIONAL INSTITUTE OF NEUROLOGICAL DISORDERS AND STROKE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

FRATAXIN; IRON; IRON SULFUR PROTEIN;

ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; CELL DEATH; EMBRYO; EMBRYO DEVELOPMENT; EXON; FRIEDREICH ATAXIA; GENE DELETION; GENE INACTIVATION; LETHALITY; MITOCHONDRION; MOUSE; NIDATION; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL;

ANIMALIA; ATAXIA;

EID: 0034192352     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/9.8.1219     Document Type: Article

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