Assembly and iron-binding properties of human frataxin, the protein dificient in Friedreich ataxia

Human Molecular Genetics

Volumn 11, Issue 3, 2002, Pages 217-227

  Cavadini, Patrizia ^a   O'Neill, Heather A ^a   Benada, Oldrich ^b   Isaya, Grazia ^a  

^a MAYO CLINIC   (United States)

^b INSTITUTE OF MICROBIOLOGY   (Czech Republic)

Author keywords

[No Author keywords available]

Indexed keywords

FRATAXIN; IRON; IRON 55; IRON BINDING PROTEIN; IRON SULFUR PROTEIN; MONOMER; PROTEIN PRECURSOR;

ANIMAL CELL; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; CONTROLLED STUDY; DEGENERATIVE DISEASE; ELECTRON MICROSCOPY; ESCHERICHIA COLI; FRIEDREICH ATAXIA; GEL FILTRATION; HEART; HUMAN; HUMAN CELL; IMMUNOPRECIPITATION; IRON BINDING CAPACITY; IRON METABOLISM; IRON TRANSPORT; ISOTOPE LABELING; MITOCHONDRION; MOLECULAR WEIGHT; MOUSE; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN BINDING; PROTEIN DEFICIENCY; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN STRUCTURE; PROTEIN SYNTHESIS; SACCHAROMYCES CEREVISIAE; STAINING; YEAST CELL;

ANIMALS; CARRIER PROTEINS; ELECTROPHORESIS, POLYACRYLAMIDE GEL; ESCHERICHIA COLI; FRIEDREICH ATAXIA; IRON; IRON-BINDING PROTEINS; MICE; MITOCHONDRIA; MYOCARDIUM; PHOSPHOTRANSFERASES (ALCOHOL GROUP ACCEPTOR); PROTEIN BINDING; RECOMBINANT PROTEINS; SACCHAROMYCES CEREVISIAE; SPECTROMETRY, MASS, ELECTROSPRAY IONIZATION; TRANSFERRIN-BINDING PROTEINS;

ANIMALIA; ESCHERICHIA COLI; SACCHAROMYCES; SACCHAROMYCES CEREVISIAE;

EID: 0036472291     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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