Reduction in frataxin causes progressive accumulation of mitochondrial damage

Human Molecular Genetics

Volumn 12, Issue 24, 2003, Pages 3331-3342

  Karthikeyan, Gopalakrishnan ^a   Santos, Janine H ^a   Graziewicz, Maria A ^a   Copeland, William C ^a   Isaya, Grazia ^b   Van Houten, Bennett ^a   Resnick, Michael A ^a  

^a NATIONAL INSTITUTE OF ENVIRONMENTAL HEALTH SCIENCES   (United States)

^b MAYO CLINIC   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CELL NUCLEUS DNA; DOUBLE STRANDED RNA; FRATAXIN; IRON; MITOCHONDRIAL DNA; MITOCHONDRIAL PROTEIN;

ARTICLE; CELL MUTANT; CONTROLLED STUDY; DISEASE COURSE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DNA DAMAGE; DNA REPAIR; DNA STRAND BREAKAGE; FRIEDREICH ATAXIA; GENE INDUCTION; GENE LOSS; GENETIC ANALYSIS; MITOCHONDRION; MOLECULAR BIOLOGY; NONHUMAN; OXIDATION; PRIORITY JOURNAL; PROMOTER REGION; REDUCTION; YEAST CELL;

CELLS, CULTURED; DNA DAMAGE; DNA, MITOCHONDRIAL; DNA-BINDING PROTEINS; DOWN-REGULATION; IRON-BINDING PROTEINS; MITOCHONDRIA; MUTATION; OXIDATION-REDUCTION; PROMOTER REGIONS (GENETICS); RAD52 DNA REPAIR AND RECOMBINATION PROTEIN; SACCHAROMYCES CEREVISIAE; SACCHAROMYCES CEREVISIAE PROTEINS;

ATAXIA;

EID: 0346752172     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/ddg349     Document Type: Article

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