Idebenone delays the onset of cardiac functional alteration without correction of Fe-S enzymes deficit in a mouse model for Friedreich ataxia

Human Molecular Genetics

Volumn 13, Issue 10, 2004, Pages 1017-1024

  Seznec, Hervé ^a   Simon, Delphine ^a   Monassier, Laurent ^b   Criqui Filipe, Paolo ^a   Gansmuller, Anne ^a   Rustin, Pierre ^c   Koening, Michel ^a   Puccio, Hélène ^a  

^a INSTITUT DE GÉNÉTIQUE ET DE BIOLOGIE MOLÉCULAIRE ET CELLULAIRE   (France)

^b INSERM   (France)

^c HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

[No Author keywords available]

Indexed keywords

FRATAXIN; IDEBENONE; IRON SULFUR PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CARDIOMYOPATHY; CONTROLLED STUDY; DISEASE COURSE; DISEASE MODEL; DRUG MECHANISM; ECHOCARDIOGRAPHY; ENZYME ACTIVITY; ENZYME INACTIVATION; FRIEDREICH ATAXIA; GENE CLUSTER; HEART DILATATION; HEART EJECTION FRACTION; HEART LEFT VENTRICLE HYPERTROPHY; HISTOPATHOLOGY; MITOCHONDRIAL RESPIRATION; MOUSE; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN ASSEMBLY; RESPIRATORY CHAIN; STATISTICAL ANALYSIS; STATISTICAL SIGNIFICANCE;

ANIMALIA;

EID: 2542556601     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/ddh114     Document Type: Article

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