A cellular model for Friedreich Ataxia revelas small-molecule glutathione peroxidase mimetics as novel treatment strategy

Human Molecular Genetics

Volumn 11, Issue 24, 2002, Pages 3055-3063

  Jauslin, Matthias L ^a   Wirth, Thomas ^b   Meier, Thomas ^a   Schoumacher, Fabrice ^a  

^a MyoContract Ltd   (Switzerland)

^b CARDIFF UNIVERSITY   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA TOCOPHEROL; ANTIOXIDANT; ASTAXANTHIN; BENZOQUINONE DERIVATIVE; BUTHIONINE SULFOXIMINE; DECYLUBIQUINONE; EBSELEN; GLUTATHIONE; GLUTATHIONE PEROXIDASE; IDEBENONE; IDEBENONE DERIVATIVE; SELENIUM; TROLOX C; UBIQUINONE DERIVATIVE; UNCLASSIFIED DRUG; DRUG DERIVATIVE; UBIDECARENONE; UBIQUINONE;

ARTICLE; CARDIOMYOPATHY; CELL ASSAY; CELL DEATH; CELL PROTECTION; CELL VIABILITY; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; DEGENERATIVE DISEASE; DETOXIFICATION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; ENZYME INHIBITION; FIBROBLAST; FRIEDREICH ATAXIA; GLUTATHIONE METABOLISM; HUMAN; HUMAN CELL; LIPOPHILICITY; PRIORITY JOURNAL; STRUCTURE ACTIVITY RELATION; BIOASSAY; BIOLOGICAL MODEL; BIOMIMETICS; BIOSYNTHESIS; ENZYMOLOGY; GENETICS; IN VITRO STUDY; METABOLISM;

ATAXIA;

BENZOQUINONES; BIOLOGICAL ASSAY; BIOMIMETICS; FIBROBLASTS; FRIEDREICH ATAXIA; GLUTATHIONE; GLUTATHIONE PEROXIDASE; HUMANS; MODELS, BIOLOGICAL; UBIQUINONE;

EID: 1842836406     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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