Iron Dysregulation in Friedreich Ataxia

Seminars in Pediatric Neurology

Volumn 13, Issue 3, 2006, Pages 166-175

  Wilson, Robert B ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

cluster; frataxin; heme; iron sulfur; mitochondria

Indexed keywords

ALPHA TOCOPHEROL; BENZOQUINONE DERIVATIVE; BUTYRIC ACID; ERYTHROPOIETIN; FRATAXIN; HEMIN; HISTONE DEACETYLASE INHIBITOR; IDEBENONE; IRON; IRON CHELATING AGENT; MANGANESE; MANGANESE SUPEROXIDE DISMUTASE; NOVOBIOCIN; OLIGODEOXYRIBONUCLEOTIDE; PYRROLE DERIVATIVE; SULFUR; UBIQUINONE;

BIOGENESIS; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FRIEDREICH ATAXIA; GENE IDENTIFICATION; GENETICS; HEME SYNTHESIS; HUMAN; IRON BINDING CAPACITY; IRON CHELATION; IRON METABOLISM; IRON OVERLOAD; MITOCHONDRIAL RESPIRATION; NONHUMAN; OXIDATIVE STRESS; PROTEIN EXPRESSION; REVIEW; SYMPTOMATOLOGY;

AMINO ACID SEQUENCE; ANIMALS; FRIEDREICH ATAXIA; HEME; HUMANS; IRON; IRON METABOLISM DISORDERS; IRON-BINDING PROTEINS; MANGANESE; MICE; MICE, KNOCKOUT; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MOLECULAR SEQUENCE DATA; OXYGEN CONSUMPTION; SULFUR; SUPEROXIDE DISMUTASE;

EID: 33750706562     PISSN: 10719091     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.spen.2006.08.005     Document Type: Review

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