Friedreich ataxia: The oxidative stress paradox

Human Molecular Genetics

Volumn 14, Issue 4, 2005, Pages 463-474

  Seznec, Hervé ^a   Simon, Delphine ^a   Bouton, Cécile ^b   Reutenauer, Laurence ^a   Hertzog, Ariane ^a   Golik, Pawel ^c   Procaccio, Vincent ^c   Patel, Manisha ^d   Drapier, Jean Claude ^b   Koenig, Michel ^a   Puccio, Hélène ^a  

^a INSTITUT DE GÉNÉTIQUE ET DE BIOLOGIE MOLÉCULAIRE ET CELLULAIRE   (France)

^b CNRS   (France)

^c UNIVERSITY OF CALIFORNIA   (United States)

^d UNIVERSITY OF COLORADO   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

5,10,15,20 TETRAKIS(4 BENZOIC ACID)PORPHYRIN; ACONITATE HYDRATASE; ANTIOXIDANT; APOLIPOPROTEIN; COPPER ZINC SUPEROXIDE DISMUTASE; FRATAXIN; HEME; IDEBENONE; IRON REGULATORY PROTEIN 1; IRON SULFUR PROTEIN; MANGANESE SUPEROXIDE DISMUTASE; RNA; SUPEROXIDE; SUPEROXIDE DISMUTASE; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANTIOXIDANT ACTIVITY; ARTICLE; CARDIOMYOPATHY; CELL DEATH; CONTROLLED STUDY; CYTOSOL; DEGENERATIVE DISEASE; DRUG MECHANISM; ENZYME ACTIVITY; FRIEDREICH ATAXIA; HEART MUSCLE CELL; IN VITRO STUDY; IRON OVERLOAD; MAMMAL CELL; MITOCHONDRION; MOUSE; NERVE CELL NECROSIS; NONHUMAN; NUCLEOTIDE SEQUENCE; OXIDATIVE STRESS; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN EXPRESSION; PROTEIN RNA BINDING; PROTEIN SYNTHESIS; SIGNAL TRANSDUCTION;

ANIMALS; BINDING SITES; CARDIOMYOPATHIES; CYTOSOL; FREE RADICAL SCAVENGERS; FRIEDREICH ATAXIA; GENE EXPRESSION PROFILING; IRON; IRON REGULATORY PROTEIN 1; IRON-SULFUR PROTEINS; MANGANESE; METALLOPORPHYRINS; MICE; MICE, KNOCKOUT; MICROARRAY ANALYSIS; MITOCHONDRIA; NEURONS; OXIDATION-REDUCTION; OXIDATIVE STRESS; RNA; SUPEROXIDE DISMUTASE;

EID: 14044273058     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/ddi042     Document Type: Article

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