Friedreich's ataxia: The vicious circle hypothesis revisited

BMC Medicine

Volumn 9, Issue , 2011, Pages

  Bayot, Aurélien ^a,b   Santos, Renata ^b   Camadro, Jean Michel ^b   Rustin, Pierre ^a,b  

^a HÔPITAL ROBERT DEBRÉ   (France)

^b UNIVERSITÉ PARIS DESCARTES   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA TOCOPHEROL; FRATAXIN; IRON; IRON SULFUR PROTEIN; OXYGEN RADICAL; REACTIVE OXYGEN METABOLITE; SUPEROXIDE; IRON BINDING PROTEIN;

ARTICLE; CLINICAL PRACTICE; FRIEDREICH ATAXIA; HUMAN; HYPERSENSITIVITY; LOSS OF FUNCTION MUTATION; NONHUMAN; PATHOPHYSIOLOGY; ANIMAL; BIOLOGICAL MODEL; GENETICS; METABOLISM; PATHOLOGY;

ANIMALS; FRIEDREICH ATAXIA; HUMANS; IRON; IRON-BINDING PROTEINS; MODELS, BIOLOGICAL; REACTIVE OXYGEN SPECIES;

EID: 80053628321     PISSN: None     EISSN: 17417015     Source Type: Journal    
DOI: 10.1186/1741-7015-9-112     Document Type: Article

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