Human iron-sulfur cluster assembly, cellular iron homeostasis, and disease

Biochemistry

Volumn 49, Issue 24, 2010, Pages 4945-4956

  Ye, Hong ^a   Rouault, Tracey A ^a  

^a EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ACONITASE; CLUSTER SYNTHESIS; CYTOSOLIC; ENZYMATIC FUNCTIONS; FRATAXIN; HUMAN DISEASE; IRON ATOMS; IRON DEFICIENCY; IRON HOMEOSTASIS; IRON-SULFUR CLUSTERS; MULTIPLE FUNCTION; PATHOPHYSIOLOGY; PROSTHETIC GROUPS; REDOX ACTIVITY; SIDEROBLASTIC ANEMIAS; SUCCINATE DEHYDROGENASE; SULFUR LIGANDS;

BIOCHEMISTRY; BODY FLUIDS; ENZYMES; GENES; REDOX REACTIONS; TISSUE;

SULFUR;

FRATAXIN; GLUTAREDOXIN; GLUTAREDOXIN 5; IRON SULFUR PROTEIN; PROTEIN ISCU; SCAFFOLD PROTEIN; UNCLASSIFIED DRUG;

BIOGENESIS; FRIEDREICH ATAXIA; GENE MUTATION; HOMEOSTASIS; HUMAN; MYOPATHY; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PRIORITY JOURNAL; PROTEIN SYNTHESIS; REVIEW; SIDEROBLASTIC ANEMIA;

ANEMIA, SIDEROBLASTIC; ANIMALS; ATP-BINDING CASSETTE TRANSPORTERS; CEREBELLAR ATAXIA; FRIEDREICH ATAXIA; GLUTAREDOXINS; HOMEOSTASIS; HUMANS; IRON; IRON-BINDING PROTEINS; IRON-SULFUR PROTEINS; MITOCHONDRIAL MYOPATHIES; MUTATION; SYNDROME;

EUKARYOTA;

EID: 77953669993     PISSN: 00062960     EISSN: 15204995     Source Type: Journal    
DOI: 10.1021/bi1004798     Document Type: Review

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