Iron and iron-responsive proteins in the cardiomyopathy of Friedreich's ataxia

Cerebellum

Volumn 5, Issue 4, 2006, Pages 257-267

  Michael, Susan ^a   Petrocine, Simone V ^b   Qian, Jiang ^b   Lamarche, Jacques B ^c   Knutson, Mitchell D ^d   Garrick, Michael D ^e   Koeppen, Arnulf H ^a,b  

^a STRATTON VA MEDICAL CENTER   (United States)

^b ALBANY MEDICAL COLLEGE   (United States)

^c CENTRE HOSPITALIER UNIVERSITAIRE DE SHERBROOKE   (Canada)

^d UNIVERSITY OF FLORIDA   (United States)

^e UNIVERSITY AT BUFFALO   (United States)

Author keywords

Cardiomyopathy; Divalent metal transporter 1; Ferritin; Ferroportin; Friedreich's ataxia; Inflammation; Iron; Mitochondrial ferritin

Indexed keywords

BISMUTH NITRATE; CD68 ANTIGEN; FERRITIN; FERROPORTIN 1; FRATAXIN; HOLOFERRITIN; IRON; IRON REGULATORY FACTOR; MESSENGER RNA; NATURAL RESISTANCE ASSOCIATED MACROPHAGE PROTEIN 2;

ADULT; AGED; ARTICLE; CLINICAL ARTICLE; CONTROLLED STUDY; CYTOSOL; ELECTRON MICROSCOPY; FEMALE; FRIEDREICH ATAXIA; HEART LEFT VENTRICLE WALL; HEART MITOCHONDRION; HEART MUSCLE CELL; HEART MUSCLE NECROSIS; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; HYPERTROPHIC CARDIOMYOPATHY; INFLAMMATORY CELL; IRON METABOLISM DISORDER; IRON RESPONSIVE ELEMENT; MALE; MUSCLE FIBRIL; MYOCARDITIS; PATHOGENESIS; PRIORITY JOURNAL; SCHOOL CHILD;

ADULT; AGE OF ONSET; AUTOPSY; CARDIOMYOPATHY, HYPERTROPHIC; ENZYME-LINKED IMMUNOSORBENT ASSAY; FEMALE; FERRITINS; FRIEDREICH ATAXIA; HUMANS; IRON; MALE; MIDDLE AGED; MYOCARDIUM; RETROSPECTIVE STUDIES;

EID: 33845337036     PISSN: 14734222     EISSN: 14734230     Source Type: Journal    
DOI: 10.1080/14734220600913246     Document Type: Article

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