Oxidative stress, mitochondrial dysfunction and cellular stress response in Friedreich's ataxia

Journal of the Neurological Sciences

Volumn 233, Issue 1-2, 2005, Pages 145-162

  Calabrese, Vittorio ^a   Lodi, Raffaele ^b   Tonon, Caterina ^b   D'Agata, Velia ^a   Sapienza, Maria ^a   Scapagnini, Giovanni ^a   Mangiameli, Andrea ^c   Pennisi, Giovanni ^c   Stella, A M Giuffrida ^a   Butterfield, D Allan ^d  

^a UNIVERSITY OF CATANIA   (Italy)

^b UNIVERSITY OF BOLOGNA   (Italy)

^c UNIVERSITY OF CATANIA   (Italy)

^d UNIVERSITY OF KENTUCKY   (United States)

Author keywords

Cell stress response; FRDA pathogenesis; MR spectroscopy; Oxidative stress

Indexed keywords

2 PYRIDYLCARBOXALDEHYDE ISONICOTINOYLHYDRAZONE; ALPHA TOCOPHEROL; ANTIOXIDANT; BILIRUBIN; CARBON MONOXIDE; CHAPERONE; CHELATING AGENT; DEFEROXAMINE; DISELENIDE; EBSELEN; FRATAXIN; FREE RADICAL; GLUTATHIONE; GLUTATHIONE PEROXIDASE; HEAT SHOCK PROTEIN; HEAT SHOCK PROTEIN 27; HEAT SHOCK PROTEIN 32; HEME OXYGENASE 1; IDEBENONE; IRON; NITRIC OXIDE; REACTIVE OXYGEN METABOLITE; SELENIDE; SELENIUM; SELENIUM DERIVATIVE; THIOL; TROLOX C; UBIDECARENONE; UNCLASSIFIED DRUG;

AGING; ALZHEIMER DISEASE; AMYOTROPHIC LATERAL SCLEROSIS; BRAIN MITOCHONDRION; CELL PROTECTION; CELL VIABILITY; CENTRAL NERVOUS SYSTEM; CLINICAL FEATURE; CONFERENCE PAPER; DEGENERATIVE DISEASE; DETOXIFICATION; DISEASE COURSE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DRUG POTENCY; ENZYME ACTIVATION; FRIEDREICH ATAXIA; GENETIC TRANSDUCTION; HEAT SHOCK RESPONSE; HUMAN; HUNTINGTON CHOREA; HYPERTHERMIA; MITOCHONDRIAL RESPIRATION; MULTIPLE SCLEROSIS; NEUROPROTECTION; NONHUMAN; NUCLEAR MAGNETIC RESONANCE IMAGING; NUCLEAR MAGNETIC RESONANCE SPECTROSCOPY; OXIDATIVE STRESS; PARKINSON DISEASE; PATHOGENESIS; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN INTERACTION; PROTEIN METABOLISM; PROTEIN SYNTHESIS; STRESS; THEORETICAL STUDY;

AGING; ANIMALS; ANTIOXIDANTS; DNA, MITOCHONDRIAL; ENERGY METABOLISM; FRIEDREICH ATAXIA; HEAT-SHOCK PROTEINS; HUMANS; MITOCHONDRIAL DISEASES; NEURODEGENERATIVE DISEASES; OXIDATIVE STRESS; REACTIVE NITROGEN SPECIES; REACTIVE OXYGEN SPECIES;

EID: 20444497908     PISSN: 0022510X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jns.2005.03.012     Document Type: Conference Paper

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