Hydrogen peroxide scavenging rescues frataxin deficiency in a Drosophila model of Friedreich's ataxia

Proceedings of the National Academy of Sciences of the United States of America

Volumn 105, Issue 2, 2008, Pages 611-616

  Anderson, Peter R ^a   Kirby, Kim ^a   Orr, William C ^b   Hilliker, Arthur J ^c   Phillips, John P ^a  

^a UNIVERSITY OF GUELPH   (Canada)

^b SOUTHERN METHODIST UNIVERSITY   (United States)

^c YORK UNIVERSITY   (Canada)

Author keywords

Catalase; Fenton chemistry; Phenotypic rescue; RNA interference

Indexed keywords

ACONITATE HYDRATASE; CATALASE; FRATAXIN; HYDROGEN PEROXIDE; PEROXIREDOXIN; REACTIVE OXYGEN METABOLITE; SUPEROXIDE;

ARTICLE; CONTROLLED STUDY; DROSOPHILA; ENZYME ACTIVITY; FRIEDREICH ATAXIA; LIFESPAN; MALE; NONHUMAN; PATHOGENESIS; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN EXPRESSION; PROTEIN FUNCTION;

ANIMALS; ANTIOXIDANTS; CATALASE; CATALYSIS; DENSITOMETRY; DISEASE MODELS, ANIMAL; DROSOPHILA MELANOGASTER; FREE RADICAL SCAVENGERS; FRIEDREICH ATAXIA; HYDROGEN PEROXIDE; IRON; IRON-BINDING PROTEINS; LONGEVITY; MITOCHONDRIA; REACTIVE OXYGEN SPECIES;

MAMMALIA;

EID: 38649103446     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.0709691105     Document Type: Article

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