A polycystin-centric view of cyst formation and disease: The polycystins revisited

Kidney International

Volumn 88, Issue 4, 2015, Pages 699-710

  Ong, Albert C M ^a   Harris, Peter C ^b  

^a UNIVERSITY OF SHEFFIELD   (United Kingdom)

^b MAYO CLINIC   (United States)

Author keywords

ADPKD; PKD1; PKD2; polycystin 1; polycystin 2; TRPP2

Indexed keywords

CALCIUM; POLYCYSTIN; POLYCYSTIN 1; POLYCYSTIN 2; POLYCYSTIC KIDNEY DISEASE 1 PROTEIN; POLYCYSTIC KIDNEY DISEASE 2 PROTEIN;

CALCIUM HOMEOSTASIS; CARBOXY TERMINAL SEQUENCE; CELL CYCLE REGULATION; CENTROSOME; CILIARY MOTILITY; COMPLEX FORMATION; DISEASE COURSE; GENE INTERACTION; HUMAN; KIDNEY POLYCYSTIC DISEASE; NONHUMAN; OLIGOMERIZATION; PRIORITY JOURNAL; PROTEIN CLEAVAGE; PROTEIN DEGRADATION; PROTEIN DEPHOSPHORYLATION; PROTEIN DOMAIN; PROTEIN FUNCTION; PROTEIN INTERACTION; PROTEIN LOCALIZATION; PROTEIN MOTIF; PROTEIN PHOSPHORYLATION; PROTEIN PROCESSING; PROTEIN TARGETING; REVIEW; SIGNAL TRANSDUCTION; UBIQUITINATION; ANIMAL; CHEMISTRY; GENETIC PREDISPOSITION; GENETICS; KIDNEY; METABOLISM; MUTATION; PATHOLOGY; PATHOPHYSIOLOGY; PHENOTYPE; POLYCYSTIC KIDNEY, AUTOSOMAL DOMINANT; PROTEIN CONFORMATION; PROTEIN TRANSPORT; STRUCTURE ACTIVITY RELATION;

ANIMALS; GENETIC PREDISPOSITION TO DISEASE; HUMANS; KIDNEY; MUTATION; PHENOTYPE; POLYCYSTIC KIDNEY, AUTOSOMAL DOMINANT; PROTEIN CONFORMATION; PROTEIN PROCESSING, POST-TRANSLATIONAL; PROTEIN TRANSPORT; SIGNAL TRANSDUCTION; STRUCTURE-ACTIVITY RELATIONSHIP; TRPP CATION CHANNELS;

EID: 84942983407     PISSN: 00852538     EISSN: 15231755     Source Type: Journal    
DOI: 10.1038/ki.2015.207     Document Type: Review

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