PRKCSH/80K-H, the protein mutated in polycystic liver disease, protects polycystin-2/TRPP2 against HERP-mediated degradation

Human Molecular Genetics

Volumn 19, Issue 1, 2009, Pages 16-24

  Gao, Hongyu ^a,b   Wang, Yan ^a   Wegierski, Tomasz ^a   Skouloudaki, Kassiani ^a   Pütz, Michael ^a   Fu, Xiao ^a   Engel, Christina ^a   Boehlke, Christopher ^a   Peng, Hongquan ^a   Kuehn, E Wolfgang ^a   Kim, Emily ^a   Kramer Zucker, Albrecht ^a   Walz, Gerd ^a,c  

^a UNIVERSITY OF FREIBURG   (Germany)

^b HUAZHONG UNIVERSITY OF SCIENCE AND TECHNOLOGY   (China)

^c UNIVERSITY OF FREIBURG   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

CELL PROTEIN; POLYCYSTIN 2; PROTEIN PRKCSH; UNCLASSIFIED DRUG; ANTISENSE OLIGONUCLEOTIDE; CARRIER PROTEIN; CHAPERONE; POLYCYSTIC KIDNEY DISEASE 2 PROTEIN; POLYCYSTIN; PRKCSH PROTEIN, ZEBRAFISH; TRPP2 PROTEIN, ZEBRAFISH; UBIQUITIN; ZEBRAFISH PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; AUTOSOMAL DOMINANT DISORDER; CARBOXY TERMINAL SEQUENCE; CONTROLLED STUDY; EMBRYO; GENE DELETION; GENE LOSS; GENE MUTATION; GENE OVEREXPRESSION; HUMAN; HUMAN CELL; KIDNEY POLYCYSTIC DISEASE; LIVER POLYCYSTIC DISEASE; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN DOMAIN; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN PROTEIN INTERACTION; SIGNAL TRANSDUCTION; SITUS INVERSUS; UBIQUITINATION; ANIMAL; ANIMAL EMBRYO; CONGENITAL MALFORMATION; DOG; DRUG EFFECT; ENDOPLASMIC RETICULUM; GENE SILENCING; GENETICS; METABOLISM; MUTATION; NEPHRON; PATHOLOGY; PRENATAL DEVELOPMENT; PROTEIN PROCESSING; ZEBRA FISH;

DANIO RERIO;

ANIMALS; CARRIER PROTEINS; DOGS; EMBRYO, NONMAMMALIAN; ENDOPLASMIC RETICULUM; GENE KNOCKDOWN TECHNIQUES; HUMANS; MOLECULAR CHAPERONES; MUTATION; NEPHRONS; OLIGONUCLEOTIDES, ANTISENSE; POLYCYSTIC KIDNEY, AUTOSOMAL DOMINANT; PROTEIN BINDING; PROTEIN PROCESSING, POST-TRANSLATIONAL; TRPP CATION CHANNELS; UBIQUITINATION; UBIQUITINS; ZEBRAFISH; ZEBRAFISH PROTEINS;

EID: 77249164094     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddp463     Document Type: Article

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