Polycystin-1 maturation requires polycystin-2 in a dose-dependent manner

Journal of Clinical Investigation

Volumn 125, Issue 2, 2015, Pages 607-620

  Gainullin, Vladimir G ^a   Hopp, Katharina ^b   Ward, Christopher J ^b   Hommerding, Cynthia J ^b   Harris, Peter C ^a,b  

^a MAYO GRADUATE SCHOOL   (United States)

^b MAYO CLINIC   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CREATININE; POLYCYSTIN 1; POLYCYSTIN 2; UREA; CHAPERONE; MULTIPROTEIN COMPLEX; POLYCYSTIC KIDNEY DISEASE 1 PROTEIN; POLYCYSTIC KIDNEY DISEASE 2 PROTEIN; POLYCYSTIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELLULAR DISTRIBUTION; CONTROLLED STUDY; CREATININE BLOOD LEVEL; DISEASE SEVERITY; ENDOPLASMIC RETICULUM; GENOTYPE; GLYCOSYLATION; HETEROZYGOTE; KIDNEY POLYCYSTIC DISEASE; MISSENSE MUTATION; MOUSE; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEPLETION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN PROCESSING; PROTEIN PROTEIN INTERACTION; UREA NITROGEN BLOOD LEVEL; ANIMAL; CELL LINE; GENETICS; KNOCKOUT MOUSE; METABOLISM; PATHOLOGY; SEVERITY OF ILLNESS INDEX;

ANIMALS; CELL LINE; ENDOPLASMIC RETICULUM; MICE; MICE, KNOCKOUT; MOLECULAR CHAPERONES; MULTIPROTEIN COMPLEXES; MUTATION, MISSENSE; POLYCYSTIC KIDNEY, AUTOSOMAL DOMINANT; SEVERITY OF ILLNESS INDEX; TRPP CATION CHANNELS;

EID: 84922157174     PISSN: 00219738     EISSN: 15588238     Source Type: Journal    
DOI: 10.1172/JCI76972     Document Type: Article

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