Lost after translation: Insights from pulmonary surfactant for understanding the role of alveolar epithelial dysfunction and cellular quality control in fibrotic lung disease

American Journal of Physiology - Lung Cellular and Molecular Physiology

Volumn 309, Issue 6, 2015, Pages L507-L525

  Mulugeta, Surafel ^a   Nureki, Shin Ichi ^b   Beers, Michael F ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b OITA UNIVERSITY   (Japan)

Author keywords

Alveolar type 2 cells; Cell quality control; Epithelial ER stress; Fibrotic lung disease; Surfactant proteins

Indexed keywords

LUNG SURFACTANT; SURFACTANT PROTEIN A; SURFACTANT PROTEIN C; SURFACTANT ASSOCIATED PROTEIN;

ALVEOLAR EPITHELIAL DYSFUNCTION; APOPTOSIS; ARTICLE; ENDOPLASMIC RETICULUM STRESS; HOMEOSTASIS; HUMAN; LUNG ALVEOLUS CELL TYPE 2; LUNG ALVEOLUS EPITHELIUM; LUNG FIBROSIS; MACROAUTOPHAGY; PATHOPHYSIOLOGY; PRIORITY JOURNAL; QUALITY CONTROL; SIGNAL TRANSDUCTION; UNFOLDED PROTEIN RESPONSE; ANIMAL; GENETICS; LUNG ALVEOLUS; LUNG ALVEOLUS CELL; METABOLISM; MUTATION; PATHOLOGY; PHYSIOLOGY; PROTEIN PROCESSING; PROTEIN TRANSPORT;

ANIMALS; APOPTOSIS; HUMANS; MUTATION; PNEUMOCYTES; PROTEIN PROCESSING, POST-TRANSLATIONAL; PROTEIN TRANSPORT; PULMONARY ALVEOLI; PULMONARY FIBROSIS; PULMONARY SURFACTANT-ASSOCIATED PROTEINS; SIGNAL TRANSDUCTION;

EID: 84941788162     PISSN: 10400605     EISSN: 15221504     Source Type: Journal    
DOI: 10.1152/ajplung.00139.2015     Document Type: Article

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