Impaired autophagy in the lipid-storage disorder niemann-pick type c1 disease

Cell Reports

Volumn 5, Issue 5, 2013, Pages 1302-1315

  Sarkar, Sovan ^a   Carroll, Bernadette ^b   Buganim, Yosef ^a   Maetzel, Dorothea ^a   Ng, AlexH M ^c   Cassady, John P ^a   Cohen, Malkiel A ^a   Chakraborty, Souvik ^d   Wang, Haoyi ^a   Spooner, Eric ^a   Ploegh, Hidde ^a   Gsponer, Joerg ^c   Korolchuk, ViktorI ^b   Jaenisch, Rudolf ^a  

^a WHITEHEAD INSTITUTE FOR BIOMEDICAL RESEARCH   (United States)

^b NEWCASTLE UNIVERSITY   (United Kingdom)

^c UNIVERSITY OF BRITISH COLUMBIA   (Canada)

^d CHILDREN S HOSPITAL OF PITTSBURGH   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BETA CYCLODEXTRIN; CELL PROTEIN; CHOLESTEROL; NPC1 PROTEIN; SNARE PROTEIN; UNCLASSIFIED DRUG;

AMPHISOME; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOPHAGOSOME; AUTOPHAGY; CELL STRUCTURE; CONTROLLED STUDY; EMBRYO; GENE; GENE MUTATION; HUMAN; HUMAN CELL; LYSOSOME; MOUSE; NIEMANN PICK DISEASE; NONHUMAN; NPC1 GENE; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN FUNCTION; RAT;

MUS;

ANIMALS; AUTOPHAGY; BETA-CYCLODEXTRINS; CELLS, CULTURED; CHOLESTEROL; HEK293 CELLS; HUMANS; LYSOSOMES; MEMBRANE GLYCOPROTEINS; MICE; NEURONS; NIEMANN-PICK DISEASE, TYPE C; RATS; SNARE PROTEINS;

EID: 84890144959     PISSN: None     EISSN: 22111247     Source Type: Journal    
DOI: 10.1016/j.celrep.2013.10.042     Document Type: Article

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