Surfactant protein C biosynthesis and its emerging role in conformational lung disease

Annual Review of Physiology

Volumn 67, Issue , 2005, Pages 663-696

  Beers, Michael F ^a   Mulugeta, Surafel ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

Apoptosis; ERAD; Interstitial pneumonia; Propeptide processing; Unfolded protein response

Indexed keywords

AMINO ACID; CASPASE; HORMONE PRECURSOR; HYBRID PROTEIN; INTEGRAL MEMBRANE PROTEIN; LUNG SURFACTANT; MEMBRANE PROTEIN; PEPTIDE; PHOSPHOLIPID; PROTEASOME; PROTEIN PRECURSOR; SURFACTANT PROTEIN C; UNCLASSIFIED DRUG;

APOPTOSIS; CELL SURVIVAL; DELETION MUTANT; DEMENTIA; ENDOPLASMIC RETICULUM; ENZYME ACTIVATION; EXOCYTOSIS; FIBROSING ALVEOLITIS; GENE MUTATION; GENE SEQUENCE; GENE STRUCTURE; IMMUNOMODULATION; LUNG ALVEOLUS CELL TYPE 2; LUNG DISEASE; LUNG PARENCHYMA; MISSENSE MUTATION; MOLECULAR MECHANICS; NUCLEOTIDE SEQUENCE; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN DOMAIN; PROTEIN FOLDING; PROTEIN ISOLATION; PROTEIN PROCESSING; PROTEIN STRUCTURE; PROTEIN SYNTHESIS; PROTEIN TARGETING; PROTEIN TRANSPORT; REGULATORY MECHANISM; REVIEW; SEQUENCE HOMOLOGY; STRUCTURE ACTIVITY RELATION;

ANIMALS; HUMANS; LUNG DISEASES; MUTATION; PULMONARY SURFACTANT-ASSOCIATED PROTEIN C; STRUCTURE-ACTIVITY RELATIONSHIP;

EID: 15544369388     PISSN: 00664278     EISSN: None     Source Type: Book Series    
DOI: 10.1146/annurev.physiol.67.040403.101937     Document Type: Review

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