BRICHOS domain associated with lung fibrosis, dementia and cancer - A chaperone that prevents amyloid fibril formation?

FEBS Journal

Volumn 278, Issue 20, 2011, Pages 3893-3904

  Willander, Hanna ^a,b   Hermansson, Erik ^b   Johansson, Jan ^a,b   Presto, Jenny ^a,b  

^a SWEDISH UNIVERSITY OF AGRICULTURAL SCIENCES   (Sweden)

^b KAROLINSKA INSTITUTE   (Sweden)

Author keywords

Alzheimer's disease; Bri; chaperone; dementia; lung fibrosis, proSP C, protein misfolding

Indexed keywords

AMYLOID; CHONDROMODULIN; CYTOKINE; GASTROKINE; MEMBRANE PROTEIN; PROSURFACTANT PROTEIN C; PROTEIN BRI1; PROTEIN BRI2; PROTEIN BRI3; PROTEIN GKN1; PROTEIN GKN2; PROTEIN GKN3; TENOMODULIN; TUMOR PROTEIN; UNCLASSIFIED DRUG;

ALZHEIMER DISEASE; AMINO TERMINAL SEQUENCE; AMYLOID PLAQUE; BRI2 GENE; BRICHOS DOMAIN; CARBOXY TERMINAL SEQUENCE; CONFERENCE PAPER; DEMENTIA; DISEASE ASSOCIATION; FAMILIAL DISEASE; GENE MUTATION; HUMAN; LUNG FIBROSIS; MOLECULAR PATHOLOGY; MUTATOR GENE; NEOPLASM; NONHUMAN; PRIORITY JOURNAL; PROSURFACTANT PROTEIN C GENE; PROTEIN BINDING; PROTEIN CLEAVAGE; PROTEIN DOMAIN; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; SIGNAL TRANSDUCTION; STRUCTURE ANALYSIS;

AMYLOID; DEMENTIA; HUMANS; MEMBRANE PROTEINS; MOLECULAR CHAPERONES; MUTATION; NEOPLASMS; PROTEIN STRUCTURE, TERTIARY; PULMONARY FIBROSIS;

EID: 80053601511     PISSN: 1742464X     EISSN: 17424658     Source Type: Journal    
DOI: 10.1111/j.1742-4658.2011.08209.x     Document Type: Conference Paper

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