Alteration of the pulmonary surfactant system in full-term infants with hereditary ABCA3 deficiency

American Journal of Respiratory and Critical Care Medicine

Volumn 174, Issue 5, 2006, Pages 571-580

  Brasch, Frank ^b   Schimanski, Sven ^b   Mühlfeld, Christian ^b   Barlage, Stefan ^b   Langmann, Thomas ^b   Aslanidis, Charalampos ^b   Boettcher, Alfred ^b   Dada, Ashraf ^b   Schroten, Horst ^b   Mildenberger, Eva ^b   Prueter, Eric ^b   Ballmann, Manfred ^b   Ochs, Matthias ^b   Johnen, Georg ^b   Griese, Matthias ^b   Schmitz, Gerd ^a  

^a UNIVERSITY OF REGENSBURG   (Germany)

^b NONE

Author keywords

ABCA3; Cathepsin D; Immunoelectron microscopy; Immunohistochemistry; Surfactant

Indexed keywords

CATHEPSIN D; LUNG SURFACTANT;

ARTICLE; CELLULAR DISTRIBUTION; CLINICAL ARTICLE; CONTROLLED STUDY; FEMALE; GENE MUTATION; GENETIC DISORDER; HUMAN; HUMAN TISSUE; IMMUNOELECTRON MICROSCOPY; IMMUNOHISTOCHEMISTRY; LUNG ALVEOLUS CELL; LUNG PARENCHYMA; MALE; NEWBORN; PRIORITY JOURNAL; PROTEIN EXPRESSION; WESTERN BLOTTING;

ATP-BINDING CASSETTE TRANSPORTERS; BRONCHOALVEOLAR LAVAGE; CASE-CONTROL STUDIES; FEMALE; HUMANS; INFANT, NEWBORN; MALE; MUTATION; PEDIGREE; PULMONARY ALVEOLI; PULMONARY SURFACTANT-ASSOCIATED PROTEINS; RESPIRATORY DISTRESS SYNDROME, NEWBORN; TERM BIRTH;

EID: 33748331188     PISSN: 1073449X     EISSN: 1073449X     Source Type: Journal    
DOI: 10.1164/rccm.200509-1535OC     Document Type: Article

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