The alveolar epithelium determines susceptibility to lung fibrosis in Hrmansky-Pdlak syndrome

American Journal of Respiratory and Critical Care Medicine

Volumn 186, Issue 10, 2012, Pages 1014-1024

  Young, Lisa R ^a   Gulleman, Peter M ^a   Bridges, James P ^b   Weaver, Timothy E ^b   Deutsch, Gail H ^c   Blackwell, Timothy S ^a   McCormack, Francis X ^d  

^a VANDERBILT UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

^c SEATTLE CHILDREN S HOSPITAL   (United States)

^d UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

Author keywords

Adaptor protein 3; Alveolar epithelial cells; Alveolar macrophage; Hermansky Pudlak syndrome; Lung fibrosis

Indexed keywords

BLEOMYCIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; BONE MARROW TRANSPLANTATION; CELL LINEAGE; CHEDIAK HIGASHI SYNDROME; CHIMERA; CONTROLLED STUDY; DISEASE PREDISPOSITION; GENE EXPRESSION; GENETIC SUSCEPTIBILITY; GENOTYPE; INTRACELLULAR SPACE; LUNG ALVEOLUS EPITHELIUM; LUNG ALVEOLUS MACROPHAGE; LUNG FIBROSIS; MACROPHAGE ACTIVATION; MOUSE; NONHUMAN; OCULAR ALBINISM; PRIORITY JOURNAL; PROTEIN EXPRESSION; WILD TYPE;

ADAPTOR PROTEIN COMPLEX 3; ANIMALS; BLEOMYCIN; GENETIC PREDISPOSITION TO DISEASE; HERMANSKI-PUDLAK SYNDROME; HUMANS; LUNG; MACROPHAGE ACTIVATION; MACROPHAGES, ALVEOLAR; MICE; MICE, KNOCKOUT; MUTATION; PROTEIN TRANSPORT; PULMONARY ALVEOLI; PULMONARY FIBROSIS; RESPIRATORY MUCOSA;

EID: 84869238694     PISSN: 1073449X     EISSN: 15354970     Source Type: Journal    
DOI: 10.1164/rccm.201207-1206OC     Document Type: Article

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