Interstitial pneumonia in Hermansky-Pudlak syndrome: Significance of florid foamy swelling/degeneration (giant lamellar body degeneration) of type-2 pneumocytes

Virchows Archiv

Volumn 437, Issue 3, 2000, Pages 304-313

  Nakatani, Y ^a   Nakamura, Nobuo ^b   Sano, Jinyu ^b   Inayama, Yoshiaki ^a   Kawano, Naomi ^a   Yamanaka, Shoji ^c   Miyagi, Yohei ^c   Nagashima, Yoji ^c   Ohbayashi, Chiho ^d   Mizushima, Mutsue ^e   Manabe, Toshiaki ^f   Kuroda, Makoto ^g   Yokoi, Toyoharu ^h   Matsubara, Osamu ⁱ  

^a YOKOHAMA CITY UNIVERSITY HOSPITAL   (Japan)

^b YOKOHAMA CITY UNIVERSITY   (Japan)

^c YOKOHAMA CITY UNIVERSITY   (Japan)

^d HYOGO MEDICAL CENTER FOR ADULTS   (Japan)

^e GIFU PREFECTURAL TAJIMI HOSPITAL   (Japan)

^f KAWASAKI MEDICAL SCHOOL   (Japan)

^g FUJITA HEALTH UNIVERSITY   (Japan)

^h NAGOYA UNIVERSITY   (Japan)

ⁱ NATIONAL DEFENSE MEDICAL COLLEGE   (Japan)

Author keywords

Giant lamellar body degeneration; Hermansky Pudlak syndrome; Interstitial pneumonia; Pulmonary fibrosis; Type 2 pneumocyte

Indexed keywords

SURFACTANT;

ADULT; ARTICLE; CELL INFILTRATION; CELL ULTRASTRUCTURE; CLINICAL ARTICLE; DISEASE ASSOCIATION; FEMALE; HISTIOCYTE; HISTOCHEMISTRY; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; INTERSTITIAL PNEUMONIA; LUNG ALVEOLUS CELL TYPE 2; LUNG BIOPSY; LUNG FIBROSIS; MACROPHAGE FUNCTION; MALE; OCULAR ALBINISM; PATHOGENESIS; PRIORITY JOURNAL;

ADULT; ALBINISM, OCULOCUTANEOUS; FEMALE; HUMANS; LUNG; LUNG DISEASES, INTERSTITIAL; MALE; MICROSCOPY, ELECTRON; MIDDLE AGED;

EID: 0033829367     PISSN: 09456317     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004280000241     Document Type: Article

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