Mitochondrial dysfunction, metabolic deficits, and increased oxidative stress in huntington's disease

Chang Gung Medical Journal

Volumn 34, Issue 2, 2011, Pages 135-152

  Chen, Chiung Mei ^a  

^a CHANG GUNG UNIVERSITY COLLEGE OF MEDICINE   (Taiwan)

Author keywords

Huntington's disease; Metabolic deficits; Mitochondrial dysfunction; Oxidative stress; Therapy

Indexed keywords

BEZAFIBRATE; CREATINE; CYCLIC AMP RESPONSIVE ELEMENT BINDING PROTEIN BINDING PROTEIN; CYCLOSPORIN A; DIMEBON; ERIODICTYOL; HUNTINGTIN; ICOSAPENTAENOIC ACID; MITOCHONDRIAL DNA; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA COACTIVATOR 1ALPHA; ROSIGLITAZONE; SUCCINATE DEHYDROGENASE (UBIQUINONE); TAUROURSODEOXYCHOLIC ACID; UBIDECARENONE; UBIQUINOL CYTOCHROME C REDUCTASE;

BIOGENESIS; BRAIN METABOLISM; CALCIUM TRANSPORT; CELL FUNCTION; DIET SUPPLEMENTATION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DRUG MECHANISM; DRUG SAFETY; DRUG TOLERABILITY; ENERGY METABOLISM; HUMAN; HUNTINGTON CHOREA; MITOCHONDRIAL PERMEABILITY; MITOCHONDRIAL RESPIRATION; NEUROIMAGING; NONHUMAN; OXIDATIVE STRESS; PATHOGENESIS; PROTEIN AGGREGATION; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN FUNCTION; PROTEIN LOCALIZATION; REVIEW; TRANSCRIPTION REGULATION; WEIGHT REDUCTION;

ANIMALS; CALCIUM; DISEASE MODELS, ANIMAL; DNA, MITOCHONDRIAL; ENERGY METABOLISM; HUMANS; HUNTINGTON DISEASE; MITOCHONDRIA; MITOCHONDRIAL MEMBRANE TRANSPORT PROTEINS; NITRO COMPOUNDS; OXIDATIVE STRESS; PROPIONIC ACIDS; TRANSCRIPTION, GENETIC;

EID: 79955930293     PISSN: 20720939     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Review

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