Mitochondrial respiration and ATP production are significantly impaired in striatal cells expressing mutant huntingtin

Journal of Biological Chemistry

Volumn 280, Issue 35, 2005, Pages 30773-30782

  Milakovic, Tamara ^a   Johnson, Gail V W ^a  

^a UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CELLS; MUTAGENESIS; PHYSIOLOGY; SUBSTRATES;

MITOCHONDRIAL DEFECTS; MITOCHONDRIAL DYSFUNCTION; MUTANT HUNTINGTIN;

ADENOSINETRIPHOSPHATE;

ADENOSINE TRIPHOSPHATE; ASCORBIC ACID; GLUTAMIC ACID; HUNTINGTIN; MALIC ACID; SUCCINIC ACID;

ANIMAL CELL; ARTICLE; CELL SPECIFICITY; COMPLEX FORMATION; CONTROLLED STUDY; EMBRYO; HUNTINGTON CHOREA; MITOCHONDRIAL DNA DISORDER; MITOCHONDRIAL RESPIRATION; MOUSE; NONHUMAN; PATHOGENESIS; PHOSPHATE TRANSPORT; PRIORITY JOURNAL; PROTEIN ANALYSIS; REGULATORY MECHANISM; WILD TYPE;

ADENOSINE TRIPHOSPHATE; ANIMALS; ANTIMYCIN A; CELL RESPIRATION; CORPUS STRIATUM; ELECTRON TRANSPORT COMPLEX I; ELECTRON TRANSPORT COMPLEX II; EMBRYO; HUMANS; HUNTINGTON DISEASE; MICE; MITOCHONDRIA; MITOCHONDRIAL PROTEINS; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; POTASSIUM CYANIDE; PROTEIN SUBUNITS; ROTENONE; UNCOUPLING AGENTS;

EID: 24744444740     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M504749200     Document Type: Article

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