Progressive dysfunction of the cholesterol biosynthesis pathway in the R6/2 mouse model of Huntington's disease

Neurobiology of Disease

Volumn 28, Issue 1, 2007, Pages 133-142

  Valenza, Marta ^a   Leoni, Valerio ^b   Tarditi, Alessia ^a   Mariotti, Caterina ^b   Björkhem, Ingeman ^c   Di Donato, Stefano ^b   Cattaneo, Elena ^a  

^a UNIVERSITY OF MILAN   (Italy)

^b DEPARTMENT OF NEUROSURGERY   (Italy)

^c KAROLINSKA UNIVERSITY HOSPITAL   (Sweden)

Author keywords

[No Author keywords available]

Indexed keywords

CHOLESTEROL; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE; LANOSTEROL; LATHOSTEROL;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CHOLESTEROL SYNTHESIS; CONTROLLED STUDY; ENZYME ACTIVITY; HUNTINGTON CHOREA; LIPID BRAIN LEVEL; METABOLIC INHIBITION; MOUSE; NONHUMAN; PRIORITY JOURNAL; TRANSGENIC MOUSE;

ANIMALS; BRAIN; CHOLESTEROL; DISEASE MODELS, ANIMAL; HUMANS; HUNTINGTON DISEASE; HYDROXYMETHYLGLUTARYL COA REDUCTASES; LANOSTEROL; MASS SPECTROMETRY; MICE; MICE, TRANSGENIC; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS;

EID: 34548777515     PISSN: 09699961     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nbd.2007.07.004     Document Type: Article

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