-
1
-
-
0028109605
-
Huntington's disease: Pathogenesis, diagnosis and treatment
-
Purdon SE, Mohr E, Ilivitsky V Jones BD (1994) Huntington's disease: pathogenesis, diagnosis and treatment. J Psychiatry Neurosci 19, 359 367.
-
(1994)
J Psychiatry Neurosci
, vol.19
, pp. 359-367
-
-
Purdon, S.E.1
Mohr, E.2
Ilivitsky, V.3
Jones, B.D.4
-
2
-
-
33846225133
-
Huntington's disease
-
Walker FO (2007) Huntington's disease. Lancet 369, 218 228.
-
(2007)
Lancet
, vol.369
, pp. 218-228
-
-
Walker, F.O.1
-
3
-
-
0030752709
-
Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain
-
DiFiglia M, Sapp E, Chase KO, Davies SW, Bates GP, Vonsattel JP Aronin N (1997) Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain. Science 277, 1990 1993.
-
(1997)
Science
, vol.277
, pp. 1990-1993
-
-
Difiglia, M.1
Sapp, E.2
Chase, K.O.3
Davies, S.W.4
Bates, G.P.5
Vonsattel, J.P.6
Aronin, N.7
-
4
-
-
0027480960
-
A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes
-
The Huntington's Disease Collaborative Research Group (
-
The Huntington's Disease Collaborative Research Group (1993) A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes. Cell 72, 971 983.
-
(1993)
Cell
, vol.72
, pp. 971-983
-
-
-
5
-
-
36949037945
-
Integrative hypothesis for Huntington's disease: A brief review on experimental evidence
-
Perez-De La Cruz V Santamaria A (2006) Integrative hypothesis for Huntington's disease: a brief review on experimental evidence. Physiol Res 56, 513 526.
-
(2006)
Physiol Res
, vol.56
, pp. 513-526
-
-
Perez-De La Cruz, V.1
Santamaria, A.2
-
6
-
-
8844220536
-
Huntingtin and the molecular pathogenesis of Huntington's disease. Fourth in molecular medicine review series
-
Landles C Bates GP (2004) Huntingtin and the molecular pathogenesis of Huntington's disease. Fourth in molecular medicine review series. EMBO Rep 5, 958 963.
-
(2004)
EMBO Rep
, vol.5
, pp. 958-963
-
-
Landles, C.1
Bates, G.P.2
-
7
-
-
0034237719
-
Energetics in the pathogenesis of neurodegenerative diseases
-
Beal MF (2000) Energetics in the pathogenesis of neurodegenerative diseases. Trends Neurosci 23, 298 304.
-
(2000)
Trends Neurosci
, vol.23
, pp. 298-304
-
-
Beal, M.F.1
-
8
-
-
0030919567
-
Oxidative damage and metabolic dysfunction in Huntington's disease: Selective vulnerability of the basal ganglia
-
Browne SE, Bowling AC, MacGarvey U, Baik MJ, Berger SC, Muqit MM, Bird ED Beal MF (1997) Oxidative damage and metabolic dysfunction in Huntington's disease: selective vulnerability of the basal ganglia. Ann Neurol 41, 646 653.
-
(1997)
Ann Neurol
, vol.41
, pp. 646-653
-
-
Browne, S.E.1
Bowling, A.C.2
MacGarvey, U.3
Baik, M.J.4
Berger, S.C.5
Muqit, M.M.6
Bird, E.D.7
Beal, M.F.8
-
9
-
-
0029875381
-
Mitochondrial defect in Huntington's disease caudate nucleus
-
Gu M, Gash MT, Mann VM, Javoy-Agid F, Cooper JM Schapira AH (1996) Mitochondrial defect in Huntington's disease caudate nucleus. Ann Neurol 39, 385 389.
-
(1996)
Ann Neurol
, vol.39
, pp. 385-389
-
-
Gu, M.1
Gash, M.T.2
Mann, V.M.3
Javoy-Agid, F.4
Cooper, J.M.5
Schapira, A.H.6
-
10
-
-
0027741301
-
Evidence for impairment of energy metabolism in vivo in Huntington's disease using localized 1H NMR spectroscopy
-
Jenkins BG, Koroshetz WJ, Beal MF Rosen BR (1993) Evidence for impairment of energy metabolism in vivo in Huntington's disease using localized 1H NMR spectroscopy. Neurology 43, 2689 2695.
-
(1993)
Neurology
, vol.43
, pp. 2689-2695
-
-
Jenkins, B.G.1
Koroshetz, W.J.2
Beal, M.F.3
Rosen, B.R.4
-
11
-
-
0033546998
-
Clinical correlation of striatal 1H MRS changes in Huntington's disease
-
Sanchez-Pernaute R, Garcia-Segura JM, del Barrio Alba A, Viano J de Yebenes JG (1999) Clinical correlation of striatal 1H MRS changes in Huntington's disease. Neurology 53, 806 812.
-
(1999)
Neurology
, vol.53
, pp. 806-812
-
-
Sanchez-Pernaute, R.1
Garcia-Segura, J.M.2
Del Barrio Alba, A.3
Viano, J.4
De Yebenes, J.G.5
-
12
-
-
0031900412
-
Quantitative proton-decoupled 31P MRS and 1H MRS in the evaluation of Huntington's and Parkinson's diseases
-
Hoang TQ, Bluml S, Dubowitz DJ, Moats R, Kopyov O, Jacques D Ross BD (1998) Quantitative proton-decoupled 31P MRS and 1H MRS in the evaluation of Huntington's and Parkinson's diseases. Neurology 50, 1033 1040.
-
(1998)
Neurology
, vol.50
, pp. 1033-1040
-
-
Hoang, T.Q.1
Bluml, S.2
Dubowitz, D.J.3
Moats, R.4
Kopyov, O.5
Jacques, D.6
Ross, B.D.7
-
13
-
-
34249112368
-
Functional imaging of cerebral blood flow and glucose metabolism in Parkinson's disease and Huntington's disease
-
Ma Y Eidelberg D (2007) Functional imaging of cerebral blood flow and glucose metabolism in Parkinson's disease and Huntington's disease. Mol Imaging Biol 9, 223 233.
-
(2007)
Mol Imaging Biol
, vol.9
, pp. 223-233
-
-
Ma, Y.1
Eidelberg, D.2
-
14
-
-
0029664992
-
Huntingtin and DRPLA proteins selectively interact with the enzyme GAPDH
-
Burke JR, Enghild JJ, Martin ME, Jou Y-S, Myers RM, Roses AD, Vance JM Strittmatter WJ (1996) Huntingtin and DRPLA proteins selectively interact with the enzyme GAPDH. Nat Med 2, 347 350.
-
(1996)
Nat Med
, vol.2
, pp. 347-350
-
-
Burke, J.R.1
Enghild, J.J.2
Martin, M.E.3
Jou, Y.-S.4
Myers, R.M.5
Roses, A.D.6
Vance, J.M.7
Strittmatter, W.J.8
-
15
-
-
0031695127
-
Brain glyceraldehyde-3-phosphate dehydrogenase activity in human trinucleotide repeat disorders
-
Kish SJ, Lopes-Cendes I, Guttman M, Furukawa Y, Pandolfo M, Rouleau GA, Ross BM, Nance M, Schut L, Ang L et al. (1998) Brain glyceraldehyde-3-phosphate dehydrogenase activity in human trinucleotide repeat disorders. Arch Neurol 55, 1299 1304.
-
(1998)
Arch Neurol
, vol.55
, pp. 1299-1304
-
-
Kish, S.J.1
Lopes-Cendes, I.2
Guttman, M.3
Furukawa, Y.4
Pandolfo, M.5
Rouleau, G.A.6
Ross, B.M.7
Nance, M.8
Schut, L.9
Ang, L.10
-
16
-
-
0031788691
-
Glyceraldehyde-3-phosphate dehydrogenase abnormality in metabolically stressed Huntington disease fibroblasts
-
Cooper AJ, Sheu KF, Burke JR, Strittmatter WJ Blass JP (1998) Glyceraldehyde-3-phosphate dehydrogenase abnormality in metabolically stressed Huntington disease fibroblasts. Dev Neurosci 20, 462 468.
-
(1998)
Dev Neurosci
, vol.20
, pp. 462-468
-
-
Cooper, A.J.1
Sheu, K.F.2
Burke, J.R.3
Strittmatter, W.J.4
Blass, J.P.5
-
17
-
-
0035145627
-
Reduction of glyceraldehyde-3-phosphate dehydrogenase activity in Alzheimer's disease and in Huntington's disease fibroblasts
-
Mazzola JL Sirover MA (2001) Reduction of glyceraldehyde-3-phosphate dehydrogenase activity in Alzheimer's disease and in Huntington's disease fibroblasts. J Neurochem 76, 442 449.
-
(2001)
J Neurochem
, vol.76
, pp. 442-449
-
-
Mazzola, J.L.1
Sirover, M.A.2
-
18
-
-
0345701435
-
Overexpression and nuclear accumulation of glyceraldehyde-3-phosphate dehydrogenase in a transgenic mouse model of Huntington's disease
-
Senatorov VV, Charles V, Reddy PH, Tagle DA Chuang DM (2003) Overexpression and nuclear accumulation of glyceraldehyde-3-phosphate dehydrogenase in a transgenic mouse model of Huntington's disease. Mol Cell Neurosci 22, 285 297.
-
(2003)
Mol Cell Neurosci
, vol.22
, pp. 285-297
-
-
Senatorov, V.V.1
Charles, V.2
Reddy, P.H.3
Tagle, D.A.4
Chuang, D.M.5
-
19
-
-
33644775636
-
Mutant huntingtin: Nuclear translocation and cytotoxicity mediated by GAPDH
-
Bae BI, Hara MR, Cascio MB, Wellington CL, Hayden MR, Ross CA, Ha HC, Li XJ, Snyder SH Sawa A (2006) Mutant huntingtin: nuclear translocation and cytotoxicity mediated by GAPDH. Proc Natl Acad Sci USA 103, 3405 3409.
-
(2006)
Proc Natl Acad Sci USA
, vol.103
, pp. 3405-3409
-
-
Bae, B.I.1
Hara, M.R.2
Cascio, M.B.3
Wellington, C.L.4
Hayden, M.R.5
Ross, C.A.6
Ha, H.C.7
Li, X.J.8
Snyder, S.H.9
Sawa, A.10
-
21
-
-
12144290495
-
Mice deficient in dihydrolipoamide dehydrogenase show increased vulnerability to MPTP, malonate and 3-nitropropionic acid neurotoxicity
-
Klivenyi P, Starkov AA, Calingasan NY, Gardian G, Browne SE, Yang L, Bubber P, Gibson GE, Patel MS Beal MF (2004) Mice deficient in dihydrolipoamide dehydrogenase show increased vulnerability to MPTP, malonate and 3-nitropropionic acid neurotoxicity. J Neurochem 88, 1352 1360.
-
(2004)
J Neurochem
, vol.88
, pp. 1352-1360
-
-
Klivenyi, P.1
Starkov, A.A.2
Calingasan, N.Y.3
Gardian, G.4
Browne, S.E.5
Yang, L.6
Bubber, P.7
Gibson, G.E.8
Patel, M.S.9
Beal, M.F.10
-
22
-
-
0032815680
-
Replicating Huntington's disease phenotype in experimental animals
-
Brouillet E, Conde F, Beal MF Hantraye P (1999) Replicating Huntington's disease phenotype in experimental animals. Prog Neurobiol 59, 427 468.
-
(1999)
Prog Neurobiol
, vol.59
, pp. 427-468
-
-
Brouillet, E.1
Conde, F.2
Beal, M.F.3
Hantraye, P.4
-
23
-
-
16044373842
-
Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotypes in transgenic mice
-
Mangiarini L, Sathasivam K, Seller M, Cozens B, Harper A, Hetherington C, Lawton M, Trottier Y, Lehrach H, Davies SW et al. (1996) Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotypes in transgenic mice. Cell 87, 493 506.
-
(1996)
Cell
, vol.87
, pp. 493-506
-
-
Mangiarini, L.1
Sathasivam, K.2
Seller, M.3
Cozens, B.4
Harper, A.5
Hetherington, C.6
Lawton, M.7
Trottier, Y.8
Lehrach, H.9
Davies, S.W.10
-
24
-
-
0033054555
-
Intranuclear inclusions and neuritic aggregates in transgenic mice expressing a mutant N-terminal fragment of huntingtin
-
Schilling G, Becher MW, Sharp AH, Jinnah HA, Duan K, Kotzuk JA, Slunt HH, Ratovitski T, Cooper JK, Jenkins NA et al. (1999) Intranuclear inclusions and neuritic aggregates in transgenic mice expressing a mutant N-terminal fragment of huntingtin. Hum Mol Genet 8, 397 407.
-
(1999)
Hum Mol Genet
, vol.8
, pp. 397-407
-
-
Schilling, G.1
Becher, M.W.2
Sharp, A.H.3
Jinnah, H.A.4
Duan, K.5
Kotzuk, J.A.6
Slunt, H.H.7
Ratovitski, T.8
Cooper, J.K.9
Jenkins, N.A.10
-
25
-
-
33244497368
-
Behaviour changes in a transgenic model of Huntington's disease
-
Klivenyi P, Bende Z, Hartai Z, Penke Z, Nemeth H, Toldi J Vecsei L (2006) Behaviour changes in a transgenic model of Huntington's disease. Behav Brain Res 169, 137 141.
-
(2006)
Behav Brain Res
, vol.169
, pp. 137-141
-
-
Klivenyi, P.1
Bende, Z.2
Hartai, Z.3
Penke, Z.4
Nemeth, H.5
Toldi, J.6
Vecsei, L.7
-
26
-
-
0028799793
-
Early loss of neostriatal striosome neurons in Huntington's disease
-
Hedreen JC Folstein SE (1995) Early loss of neostriatal striosome neurons in Huntington's disease. J Neuropathol Exp Neurol 54, 105 120.
-
(1995)
J Neuropathol Exp Neurol
, vol.54
, pp. 105-120
-
-
Hedreen, J.C.1
Folstein, S.E.2
-
27
-
-
0033857139
-
Can yeast glycolysis be understood in terms of in vitro kinetics of the constituent enzymes? Testing biochemistry
-
Teusink B, Passarge J, Reijenga CA, Esgalhado E, van der Weijden CC, Schepper M, Walsh MC, Bakker BM, van Dam K, Westerhoff HV et al. (2000) Can yeast glycolysis be understood in terms of in vitro kinetics of the constituent enzymes? Testing biochemistry. Eur J Biochem 267, 5313 5329.
-
(2000)
Eur J Biochem
, vol.267
, pp. 5313-5329
-
-
Teusink, B.1
Passarge, J.2
Reijenga, C.A.3
Esgalhado, E.4
Van Der Weijden, C.C.5
Schepper, M.6
Walsh, M.C.7
Bakker, B.M.8
Van Dam, K.9
Westerhoff, H.V.10
-
29
-
-
62049085905
-
Systems biology towards life in silico: Mathematics of the control of living cells
-
[Epub ahead of print].
-
Westerhoff HV, Kolodkin A, Conradie R, Wilkinson SJ, Bruggeman FJ, Krab K, van Schuppen JH, Hardin H, Bakker BM, Moné MJ et al. (2008) Systems biology towards life in silico: mathematics of the control of living cells. J Math Biol [Epub ahead of print].
-
(2008)
J Math Biol
-
-
Westerhoff, H.V.1
Kolodkin, A.2
Conradie, R.3
Wilkinson, S.J.4
Bruggeman, F.J.5
Krab, K.6
Van Schuppen, J.H.7
Hardin, H.8
Bakker, B.M.9
Moné, M.J.10
-
30
-
-
0142038896
-
Intracellular energy failure does not underlie hyperthermic spreading depressions in immature rat hippocampal slice
-
Wu J, Takeo T, Wakui M, Ellsworth K Fisher RS (2003) Intracellular energy failure does not underlie hyperthermic spreading depressions in immature rat hippocampal slice. Brain Res 987, 240 243.
-
(2003)
Brain Res
, vol.987
, pp. 240-243
-
-
Wu, J.1
Takeo, T.2
Wakui, M.3
Ellsworth, K.4
Fisher, R.S.5
-
31
-
-
0036429377
-
A model of the coupling between brain electrical activity, metabolism, and hemodynamics: Application to the interpretation of functional neuroimaging
-
Aubert A Costalat R (2002) A model of the coupling between brain electrical activity, metabolism, and hemodynamics: application to the interpretation of functional neuroimaging. Neuroimage 17, 1162 1181.
-
(2002)
Neuroimage
, vol.17
, pp. 1162-1181
-
-
Aubert, A.1
Costalat, R.2
-
32
-
-
0034329159
-
Molecular genetics: Unmasking polyglutamine triggers in neurodegenerative disease
-
Gusella JF MacDonald ME (2000) Molecular genetics: unmasking polyglutamine triggers in neurodegenerative disease. Nat Rev Neurosci 1, 109 115.
-
(2000)
Nat Rev Neurosci
, vol.1
, pp. 109-115
-
-
Gusella, J.F.1
MacDonald, M.E.2
-
33
-
-
7244236320
-
Inclusion body formation reduces levels of mutant huntingtin and the risk of neuronal death
-
Arrasate M, Mitra S, Schweitzer ES, Segal MR Finkbeiner S (2004) Inclusion body formation reduces levels of mutant huntingtin and the risk of neuronal death. Nature 431, 805 810.
-
(2004)
Nature
, vol.431
, pp. 805-810
-
-
Arrasate, M.1
Mitra, S.2
Schweitzer, E.S.3
Segal, M.R.4
Finkbeiner, S.5
-
34
-
-
10344233758
-
Mitochondrial dysfunction measured in vivo
-
Marcinek DJ (2004) Mitochondrial dysfunction measured in vivo. Acta Physiol Scand 182, 343 352.
-
(2004)
Acta Physiol Scand
, vol.182
, pp. 343-352
-
-
Marcinek, D.J.1
-
35
-
-
26444441008
-
HD CAG repeat implicates a dominant property of huntingtin in mitochondrial energy metabolism
-
Seong IS, Ivanova E, Lee JM, Choo YS, Fossale E, Anderson M, Gusella JF, Laramie JM, Myers RH, Lesort M et al. (2005) HD CAG repeat implicates a dominant property of huntingtin in mitochondrial energy metabolism. Hum Mol Genet 14, 2871 2880.
-
(2005)
Hum Mol Genet
, vol.14
, pp. 2871-2880
-
-
Seong, I.S.1
Ivanova, E.2
Lee, J.M.3
Choo, Y.S.4
Fossale, E.5
Anderson, M.6
Gusella, J.F.7
Laramie, J.M.8
Myers, R.H.9
Lesort, M.10
-
36
-
-
29244483093
-
Effect of coenzyme Q10 and vitamin e on brain energy metabolism in the animal model of Huntington's disease
-
Kasparová S, Sumbalová Z, Bystrický P, Kucharská J, Liptaj T, Mlynárik V Gvozdjáková A (2006) Effect of coenzyme Q10 and vitamin E on brain energy metabolism in the animal model of Huntington's disease. Neurochem Int 48, 93 99.
-
(2006)
Neurochem Int
, vol.48
, pp. 93-99
-
-
Kasparová, S.1
Sumbalová, Z.2
Bystrický, P.3
Kucharská, J.4
Liptaj, T.5
Mlynárik, V.6
Gvozdjáková, A.7
-
37
-
-
0034743672
-
Creatine increase survival and delays motor symptoms in a transgenic animal model of Huntington's disease
-
Andreassen OA, Dedeoglu A, Ferrante RJ, Jenkins BG, Ferrante KL, Thomas M, Friedlich A, Browne SE, Schilling G, Borchelt DR et al. (2001) Creatine increase survival and delays motor symptoms in a transgenic animal model of Huntington's disease. Neurobiol Dis 8, 479 491.
-
(2001)
Neurobiol Dis
, vol.8
, pp. 479-491
-
-
Andreassen, O.A.1
Dedeoglu, A.2
Ferrante, R.J.3
Jenkins, B.G.4
Ferrante, K.L.5
Thomas, M.6
Friedlich, A.7
Browne, S.E.8
Schilling, G.9
Borchelt, D.R.10
-
38
-
-
0031964359
-
Neuroprotective effects of creatine and cyclocreatine in animal models of Huntington's disease
-
Matthews RT, Yang L, Jenkins BG, Ferrante RJ, Rosen BR, Kaddurah-Daouk R Beal MF (1998) Neuroprotective effects of creatine and cyclocreatine in animal models of Huntington's disease. J Neurosci 18, 156 163.
-
(1998)
J Neurosci
, vol.18
, pp. 156-163
-
-
Matthews, R.T.1
Yang, L.2
Jenkins, B.G.3
Ferrante, R.J.4
Rosen, B.R.5
Kaddurah-Daouk, R.6
Beal, M.F.7
-
39
-
-
36549050391
-
Increased metabolism in the R6/2 mouse model of Huntington's disease
-
van der Burg JM, Bacos K, Wood NI, Lindqvist A, Wierup N, Woodman B, Wamsteeker JI, Smith R, Deierborg T, Kuhar MJ et al. (2008) Increased metabolism in the R6/2 mouse model of Huntington's disease. Neurobiol Dis 29, 41 51.
-
(2008)
Neurobiol Dis
, vol.29
, pp. 41-51
-
-
Van Der Burg, J.M.1
Bacos, K.2
Wood, N.I.3
Lindqvist, A.4
Wierup, N.5
Woodman, B.6
Wamsteeker, J.I.7
Smith, R.8
Deierborg, T.9
Kuhar, M.J.10
-
41
-
-
26844550967
-
Effects of CAG repeat length, HTT protein length and protein context on cerebral metabolism measured using magnetic resonance spectroscopy in transgenic mouse models of Huntington's disease
-
Jenkins BG, Andreassen OA, Dedeoglu A, Leavitt B, Hayden M, Borchelt D, Ross CA, Ferrante RJ Beal MF (2005) Effects of CAG repeat length, HTT protein length and protein context on cerebral metabolism measured using magnetic resonance spectroscopy in transgenic mouse models of Huntington's disease. J Neurochem 95, 553 562.
-
(2005)
J Neurochem
, vol.95
, pp. 553-562
-
-
Jenkins, B.G.1
Andreassen, O.A.2
Dedeoglu, A.3
Leavitt, B.4
Hayden, M.5
Borchelt, D.6
Ross, C.A.7
Ferrante, R.J.8
Beal, M.F.9
-
42
-
-
0034006477
-
Nonlinear decrease over time in N-acetyl aspartate levels in the absence of neuronal loss and increases in glutamine and glucose in transgenic Huntington's disease mice
-
Jenkins BG, Klivenyi P, Kustermann E, Andreassen OA, Ferrante RJ, Rosen BR Beal MF (2000) Nonlinear decrease over time in N-acetyl aspartate levels in the absence of neuronal loss and increases in glutamine and glucose in transgenic Huntington's disease mice. J Neurochem 74, 2108 2119.
-
(2000)
J Neurochem
, vol.74
, pp. 2108-2119
-
-
Jenkins, B.G.1
Klivenyi, P.2
Kustermann, E.3
Andreassen, O.A.4
Ferrante, R.J.5
Rosen, B.R.6
Beal, M.F.7
-
43
-
-
0034994207
-
Early degenerative changes in transgenic mice expressing mutant huntingtin involve dendritic abnormalities but no impairment of mitochondrial energy production
-
Guidetti P, Charles V, Chen EY, Reddy PH, Kordower JH, Whetsell WOJ, Schwarcz R Tagle DA (2001) Early degenerative changes in transgenic mice expressing mutant huntingtin involve dendritic abnormalities but no impairment of mitochondrial energy production. Exp Neurol 169, 340 350.
-
(2001)
Exp Neurol
, vol.169
, pp. 340-350
-
-
Guidetti, P.1
Charles, V.2
Chen, E.Y.3
Reddy, P.H.4
Kordower, J.H.5
Whetsell, W.O.J.6
Schwarcz, R.7
Tagle, D.A.8
-
44
-
-
10744226789
-
Neuronal vulnerability following inhibition of mitochondrial complex II: A possible ionic mechanism for Huntington's disease
-
Saulle E, Gubellini P, Picconi B, Centonze D, Tropepi D, Pisani A, Morari M, Marti M, Rossi L, Papa M et al. (2004) Neuronal vulnerability following inhibition of mitochondrial complex II: a possible ionic mechanism for Huntington's disease. Mol Cell Neurosci 25, 9 20.
-
(2004)
Mol Cell Neurosci
, vol.25
, pp. 9-20
-
-
Saulle, E.1
Gubellini, P.2
Picconi, B.3
Centonze, D.4
Tropepi, D.5
Pisani, A.6
Morari, M.7
Marti, M.8
Rossi, L.9
Papa, M.10
-
45
-
-
51749093777
-
Energy metabolism in conformational diseases
-
In. Bertau, M., Mosekilde, E. Westerhoff, H., eds. pp. Wiley, Weinheim.
-
Ovádi J Orosz F (2007) Energy metabolism in conformational diseases. In Biosimulation in Drug Development (Bertau M, Mosekilde E Westerhoff H, eds pp. 233 257. Wiley, Weinheim.
-
(2007)
Biosimulation in Drug Development
, pp. 233-257
-
-
Ovádi, J.1
Orosz, F.2
-
46
-
-
0035478762
-
Do active cerebral neurons really use lactate rather than glucose?
-
Chih CP, Lipton P Roberts ELJ (2001) Do active cerebral neurons really use lactate rather than glucose? Trends Neurosci 24, 573 578.
-
(2001)
Trends Neurosci
, vol.24
, pp. 573-578
-
-
Chih, C.P.1
Lipton, P.2
Roberts, E.L.J.3
-
47
-
-
0028080101
-
Glutamate uptake into astrocytes stimulates aerobic glycolysis: A mechanism coupling neuronal activity to glucose utilization
-
Pellerin L Magistretti PJ (1994) Glutamate uptake into astrocytes stimulates aerobic glycolysis: a mechanism coupling neuronal activity to glucose utilization. Proc Natl Acad Sci USA 91, 10625 10629.
-
(1994)
Proc Natl Acad Sci USA
, vol.91
, pp. 10625-10629
-
-
Pellerin, L.1
Magistretti, P.J.2
-
48
-
-
33847788629
-
Imaging microglial activation in Huntington's disease
-
Tai YF, Pavese N, Gerhard A, Tabrizi SJ, Barker RA, Brooks DJ Piccini P (2007) Imaging microglial activation in Huntington's disease. Brain Res Bull 72, 148 151.
-
(2007)
Brain Res Bull
, vol.72
, pp. 148-151
-
-
Tai, Y.F.1
Pavese, N.2
Gerhard, A.3
Tabrizi, S.J.4
Barker, R.A.5
Brooks, D.J.6
Piccini, P.7
-
49
-
-
0035909948
-
Different responses of astrocytes and neurons to nitric oxide: The role of glycolytically generated ATP in astrocyte protection
-
Almeida A, Almeida J, Bolanos JP Moncada S (2001) Different responses of astrocytes and neurons to nitric oxide: the role of glycolytically generated ATP in astrocyte protection. Proc Natl Acad Sci USA 98, 15294 15299.
-
(2001)
Proc Natl Acad Sci USA
, vol.98
, pp. 15294-15299
-
-
Almeida, A.1
Almeida, J.2
Bolanos, J.P.3
Moncada, S.4
-
50
-
-
0017184389
-
A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding
-
Bradford MM (1976) A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding. Anal Biochem 72, 248 254.
-
(1976)
Anal Biochem
, vol.72
, pp. 248-254
-
-
Bradford, M.M.1
-
51
-
-
0017347447
-
International Committee for Standardization in Haematology: Recommended methods for red-cell enzyme analysis
-
Beutler E, Blume KG, Kaplan JC, Löhr GW, Ramot B Valentine WN (1977) International Committee for Standardization in Haematology: recommended methods for red-cell enzyme analysis. Br J Haematol 35, 331 340.
-
(1977)
Br J Haematol
, vol.35
, pp. 331-340
-
-
Beutler, E.1
Blume, K.G.2
Kaplan, J.C.3
Löhr, G.W.4
Ramot, B.5
Valentine, W.N.6
-
52
-
-
0032486399
-
Human xenomitochondrial cybrids. Cellular models of mitochondrial complex I deficiency
-
Barrientos A, Kenyon L Moraes CT (1998) Human xenomitochondrial cybrids. Cellular models of mitochondrial complex I deficiency. J Biol Chem 273, 14210 14217.
-
(1998)
J Biol Chem
, vol.273
, pp. 14210-14217
-
-
Barrientos, A.1
Kenyon, L.2
Moraes, C.T.3
|