Oxidative stress, mitochondrial and proteostasis malfunction in adrenoleukodystrophy: A paradigm for axonal degeneration

Free Radical Biology and Medicine

Volumn 88, Issue , 2015, Pages 18-29

  Fourcade, Stéphane ^a,b,c   Ferrer, Isidre ^b,d   Pujol, Aurora ^a,b,c,e  

^a BELLVITGE BIOMEDICAL RESEARCH INSTITUTE IDIBELL   (Spain)

^b HOSPITAL UNIVERSITARI DE BELLVITGE   (Spain)

^c CENTRO DE INVESTIGACIÓN BIOMÉDICA EN RED DE ENFERMEDADES RARAS CIBERER   (Spain)

^d CENTRO DE INVESTIGACIÓN BIOMÉDICA EN RED SOBRE ENFERMEDADES NEURODEGENERATIVAS CIBERNED   (Spain)

^e INSTITUCIÓ CATALANA DE RECERCA I ESTUDIS AVANÇATS ICREA   (Spain)

Author keywords

Autophagy; Mitochondrial dysfunction; Oxidative damage; Peroxisome; Proteasome; Very long chain fatty acids; X linked adrenoleukodystrophy

Indexed keywords

MAMMALIAN TARGET OF RAPAMYCIN; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA COACTIVATOR 1ALPHA; PROTEASOME; SIRTUIN 1; UBIQUITIN; VERY LONG CHAIN FATTY ACID;

ADRENOLEUKODYSTROPHY; AUTOPHAGY; BIOGENESIS; CELL AGING; CELL SURVIVAL; CITRIC ACID CYCLE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; GLYCOLYSIS; HUMAN; LIPID PEROXIDATION; LOSS OF FUNCTION MUTATION; MICROENVIRONMENT; MITOCHONDRIAL MEMBRANE; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL RESPIRATION; NERVE CELL; NERVE DEGENERATION; NERVE FIBER DEGENERATION; NONHUMAN; OLIGODENDROGLIA; OXIDATION REDUCTION STATE; OXIDATIVE PHOSPHORYLATION; OXIDATIVE STRESS; PEROXISOME; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN HOMEOSTASIS; PROTEIN QUALITY; REVIEW; ANIMAL; AXON; COMPLICATION; DISEASE MODEL; METABOLISM; MITOCHONDRION; MOUSE; NEURODEGENERATIVE DISEASES; PATHOPHYSIOLOGY; PROTEOSTASIS DEFICIENCIES;

ADRENOLEUKODYSTROPHY; ANIMALS; AXONS; DISEASE MODELS, ANIMAL; HUMANS; MICE; MITOCHONDRIA; NEURODEGENERATIVE DISEASES; OXIDATIVE STRESS; PEROXISOMES; PROTEOSTASIS DEFICIENCIES;

EID: 84942985045     PISSN: 08915849     EISSN: 18734596     Source Type: Journal    
DOI: 10.1016/j.freeradbiomed.2015.05.041     Document Type: Review

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