-
2
-
-
0001687866
-
The peroxisome biogenesis disorders
-
Scriver CR, Beaudet AL, Valle D, and Sly WS, eds. New York: McGraw-Hill
-
Gould SJ, Raymond GV, Valle D. The peroxisome biogenesis disorders. In: Scriver CR, Beaudet AL, Valle D, and Sly WS, eds. The Metabolic and Molecular Bases of Inherited Disease. New York: McGraw-Hill, 2001:3181-3217.
-
(2001)
The Metabolic and Molecular Bases of Inherited Disease
, pp. 3181-3217
-
-
Gould, S.J.1
Raymond, G.V.2
Valle, D.3
-
3
-
-
0021047742
-
The cerebrohepatorenal syndrome of Zellweger, morphologic and metabolic aspects
-
Kelley RI. The cerebrohepatorenal syndrome of Zellweger, morphologic and metabolic aspects. Am J Med Genet 1983;16:503-517.
-
(1983)
Am J Med Genet
, vol.16
, pp. 503-517
-
-
Kelley, R.I.1
-
4
-
-
0015848845
-
Peroxisomal and mitochondrial defects in the cerebro-hepato-renal syndrome
-
Goldfischer S, Moore CL, Johnson AB, Spiro AJ, Valsamis MP, Wisniewski HK, et al. Peroxisomal and mitochondrial defects in the cerebro-hepato-renal syndrome. Science 1973;182:62-64.
-
(1973)
Science
, vol.182
, pp. 62-64
-
-
Goldfischer, S.1
Moore, C.L.2
Johnson, A.B.3
Spiro, A.J.4
Valsamis, M.P.5
Wisniewski, H.K.6
-
5
-
-
0020582364
-
Biochemical studies in the liver and muscle of patients with Zellweger syndrome
-
Trijbels JMF, Berden JA, Monnens LAH, Willems JL, Janssen AJM, Schutgens RBH, et al. Biochemical studies in the liver and muscle of patients with Zellweger syndrome. Pediatr Res 1983;17:514-517.
-
(1983)
Pediatr Res
, vol.17
, pp. 514-517
-
-
Trijbels, J.M.F.1
Berden, J.A.2
Monnens, L.A.H.3
Willems, J.L.4
Janssen, A.J.M.5
Schutgens, R.B.H.6
-
6
-
-
0019168913
-
Liver in the cerebro-hepato-renal syndrome: Defective bile acid synthesis and abnormal mitochondria
-
Mathis RK, Watkins JB, Szczepanik-Van Leeuwen P, Lott IT. Liver in the cerebro-hepato-renal syndrome: defective bile acid synthesis and abnormal mitochondria. Gastroenterology 1980;79:1311-1317.
-
(1980)
Gastroenterology
, vol.79
, pp. 1311-1317
-
-
Mathis, R.K.1
Watkins, J.B.2
Szczepanik-Van Leeuwen, P.3
Lott, I.T.4
-
7
-
-
0025089946
-
Pathology of hepatic peroxisomes and mitochondria in patients with peroxisomal disorders
-
Hughes JL, Poulos A, Robertson E, Chow CW, Sheffield LJ, Christodoulou J. Pathology of hepatic peroxisomes and mitochondria in patients with peroxisomal disorders. Virchows Arch A Pathol Anat Histol 1990;416:255-264.
-
(1990)
Virchows Arch A Pathol Anat Histol
, vol.416
, pp. 255-264
-
-
Hughes, J.L.1
Poulos, A.2
Robertson, E.3
Chow, C.W.4
Sheffield, L.J.5
Christodoulou, J.6
-
8
-
-
0018712604
-
Licht- und elektronenmikroskopische leberbefunde beim cerebro-hepato-renalen syndrom nach zellweger (peroxisomen-defizienz)
-
Pfeifer U, Sandhage K. Licht- und Elektronenmikroskopische Leberbefunde beim Cerebro-Hepato-renalen Syndrom nach Zellweger (Peroxisomen-Defizienz). Virchows Arch A Pathol Anat Histol 1979:384:269-284.
-
(1979)
Virchows Arch A Pathol Anat Histol
, vol.384
, pp. 269-284
-
-
Pfeifer, U.1
Sandhage, K.2
-
9
-
-
0020973652
-
Ultrastructure of the liver in the cerebrohepatorenal syndrome of Zellweger
-
Mooi WJ, Dingemans KP, Van den Bergh Weerman MA, Jöbsis AC, Heymans HAS, Barth PG. Ultrastructure of the liver in the cerebrohepatorenal syndrome of Zellweger. Ultrastruct Pathol 1983;5:135-144.
-
(1983)
Ultrastruct Pathol
, vol.5
, pp. 135-144
-
-
Mooi, W.J.1
Dingemans, K.P.2
Van Den Bergh Weerman, M.A.3
Jöbsis, A.C.4
Heymans, H.A.S.5
Barth, P.G.6
-
10
-
-
0015843704
-
Peroxisomal abnormalities in metabolic diseases
-
Goldfischer S, Johnson AB, Essner E, Moore C, Ritch RH. Peroxisomal abnormalities in metabolic diseases. J Histochem Cytochem 1997;21:972-977.
-
(1997)
J Histochem Cytochem
, vol.21
, pp. 972-977
-
-
Goldfischer, S.1
Johnson, A.B.2
Essner, E.3
Moore, C.4
Ritch, R.H.5
-
11
-
-
0021871792
-
The cerebrohepato-renal (Zellweger) syndrome: Lamellar lipid profiles in adrenocortical, hepatic mesenchymal, astrocyte cells and increased levels of very long chain fatty acids and phytanic acid in the plasma
-
Aubourg P, Robain O, Rocchiccioli F, Dancea S, Scotto J. The cerebrohepato-renal (Zellweger) syndrome: lamellar lipid profiles in adrenocortical, hepatic mesenchymal, astrocyte cells and increased levels of very long chain fatty acids and phytanic acid in the plasma. J Neurol Sci 1985;69:9-25.
-
(1985)
J Neurol Sci
, vol.69
, pp. 9-25
-
-
Aubourg, P.1
Robain, O.2
Rocchiccioli, F.3
Dancea, S.4
Scotto, J.5
-
12
-
-
0022412223
-
Zellweger syndrome: Biochemical and morphological studies on two patients treated with clofibrate
-
Lazarow PB, Black V, Shio H, Fujiki Y, Hajra AK, Datta NS, et al. Zellweger syndrome: biochemical and morphological studies on two patients treated with clofibrate. Pediatr Res 1985;19:1356-1364.
-
(1985)
Pediatr Res
, vol.19
, pp. 1356-1364
-
-
Lazarow, P.B.1
Black, V.2
Shio, H.3
Fujiki, Y.4
Hajra, A.K.5
Datta, N.S.6
-
13
-
-
16944361876
-
A mouse model for Zellweger syndrome
-
Baes M, Gressens P, Baumgart E, Carmeliet P, Casteels M, Fransen M, et al. A mouse model for Zellweger syndrome. Nat Genet 1997;17:49-57.
-
(1997)
Nat Genet
, vol.17
, pp. 49-57
-
-
Baes, M.1
Gressens, P.2
Baumgart, E.3
Carmeliet, P.4
Casteels, M.5
Fransen, M.6
-
14
-
-
0034799180
-
Mitochondrial alterations caused by defective peroxisomal biogenesis in a mouse model for Zellweger syndrome (PEX5 knockout mouse)
-
Baumgart E, Vanhorebeek I, Grabenbauer M, Borgers M, Declercq P, Fahimi HD, et al. Mitochondrial alterations caused by defective peroxisomal biogenesis in a mouse model for Zellweger syndrome (PEX5 knockout mouse). Am J Pathol 2001;159:1477-1494.
-
(2001)
Am J Pathol
, vol.159
, pp. 1477-1494
-
-
Baumgart, E.1
Vanhorebeek, I.2
Grabenbauer, M.3
Borgers, M.4
Declercq, P.5
Fahimi, H.D.6
-
15
-
-
0032898369
-
Dual roles for glucokinase in glucose homeostasis as determined by liver and pancreatic β cell-specific gene knock-outs using Cre recombinase
-
Postic C, Shiota M, Niswender KD, Jetton TL, Chen Y, Moates JM, et al. Dual roles for glucokinase in glucose homeostasis as determined by liver and pancreatic β cell-specific gene knock-outs using Cre recombinase. J Biol Chem 1999:274:305-315.
-
(1999)
J Biol Chem
, vol.274
, pp. 305-315
-
-
Postic, C.1
Shiota, M.2
Niswender, K.D.3
Jetton, T.L.4
Chen, Y.5
Moates, J.M.6
-
16
-
-
0036198394
-
Generation of Pex5-IoxP mice allowing the conditional elimination of peroxisomes
-
Baes M, Dewerchin M, Janssen A, Collen D, Carmeliet P. Generation of Pex5-IoxP mice allowing the conditional elimination of peroxisomes. Genesis 2002;32:177-178.
-
(2002)
Genesis
, vol.32
, pp. 177-178
-
-
Baes, M.1
Dewerchin, M.2
Janssen, A.3
Collen, D.4
Carmeliet, P.5
-
17
-
-
0035252794
-
Prenatal and postnatal development of peroxisomal lipid-metabolizing pathways in the mouse
-
Huyghe S, Casteels M, Janssen A, Meulders L, Mannaerts GP, Declercq PE, et al. Prenatal and postnatal development of peroxisomal lipid-metabolizing pathways in the mouse. Biochem J 2001;353:673-680.
-
(2001)
Biochem J
, vol.353
, pp. 673-680
-
-
Huyghe, S.1
Casteels, M.2
Janssen, A.3
Meulders, L.4
Mannaerts, G.P.5
Declercq, P.E.6
-
18
-
-
0027960215
-
Superoxide and peroxynitrite inactivate aconitases, but nitric oxide does not
-
Hausladen A, Fridovich I. Superoxide and peroxynitrite inactivate aconitases, but nitric oxide does not. J Biol Chem 1994;269:29405-29408.
-
(1994)
J Biol Chem
, vol.269
, pp. 29405-29408
-
-
Hausladen, A.1
Fridovich, I.2
-
19
-
-
0019740345
-
Assay of glutathione, glutathione disulfide, and glutathione mixed disulfides in biological samples
-
Akerboom TPM, Sies H. Assay of glutathione, glutathione disulfide, and glutathione mixed disulfides in biological samples. Methods Enzymol 1981;77:373-382.
-
(1981)
Methods Enzymol
, vol.77
, pp. 373-382
-
-
Akerboom, T.P.M.1
Sies, H.2
-
20
-
-
0030722559
-
The tetrazolium dyes MTS and XTT provide new quantitative assays for superoxide and superoxide dismutase
-
Sutherland MW, Learmonth BA. The tetrazolium dyes MTS and XTT provide new quantitative assays for superoxide and superoxide dismutase. Free Radic Res 1997;27:283-289.
-
(1997)
Free Radic Res
, vol.27
, pp. 283-289
-
-
Sutherland, M.W.1
Learmonth, B.A.2
-
21
-
-
0023664229
-
Permeability of the peroxisomal membrane to cofactors of β-oxidation
-
Van Veldhoven PP, Just WW, Mannaerts GP. Permeability of the peroxisomal membrane to cofactors of β-oxidation, J Biol Chem 1987;262: 4310-4318.
-
(1987)
J Biol Chem
, vol.262
, pp. 4310-4318
-
-
Van Veldhoven, P.P.1
Just, W.W.2
Mannaerts, G.P.3
-
22
-
-
0023201142
-
Lipoperoxides in plasma as measured by liquid-chromatographic separation of malondialdehyde-thiobarbituric acid adduct
-
Wong SHY, Knight JA, Hopfer SM, Zaharia O, Leach CN, Sunderman FW. Lipoperoxides in plasma as measured by liquid-chromatographic separation of malondialdehyde-thiobarbituric acid adduct. Clin Chem 1987;33:214-220.
-
(1987)
Clin Chem
, vol.33
, pp. 214-220
-
-
Wong, S.H.Y.1
Knight, J.A.2
Hopfer, S.M.3
Zaharia, O.4
Leach, C.N.5
Sunderman, F.W.6
-
23
-
-
0025102226
-
Determination of carbonyl content in oxidatively modified proteins
-
Levine RL, Garland D, Oliver CN, Amici A, Lenz AG, Ahn BW, et al. Determination of carbonyl content in oxidatively modified proteins. Methods Enzymol 1990;186:464-478.
-
(1990)
Methods Enzymol
, vol.186
, pp. 464-478
-
-
Levine, R.L.1
Garland, D.2
Oliver, C.N.3
Amici, A.4
Lenz, A.G.5
Ahn, B.W.6
-
24
-
-
0023154010
-
Factors underlying significant underestimation of glucokinase activity in crude liver extracts: Physiological implications of higher cellular activity
-
Davidson AL, Arion WJ. Factors underlying significant underestimation of glucokinase activity in crude liver extracts: physiological implications of higher cellular activity. Arch Biochem Biophys 1987:253:156-157.
-
(1987)
Arch Biochem Biophys
, vol.253
, pp. 156-157
-
-
Davidson, A.L.1
Arion, W.J.2
-
25
-
-
0020392647
-
Pyruvate kinase isoenzymes from rat
-
Imamura K, Tanaka T. Pyruvate kinase isoenzymes from rat. Methods Enzymol 1982;90:150-165.
-
(1982)
Methods Enzymol
, vol.90
, pp. 150-165
-
-
Imamura, K.1
Tanaka, T.2
-
26
-
-
0036204534
-
The neuronal migration defect in mice with Zellweger syndrome (Pex5 knockout) is not caused by the inactivity of peroxisomal β-oxidation
-
Baes M, Gressens P, Huyghe S, De Nys K, Qi C, Jia Y, et al. The neuronal migration defect in mice with Zellweger syndrome (Pex5 knockout) is not caused by the inactivity of peroxisomal β-oxidation. J Neuropath Exp Neur 2002;61:368-374.
-
(2002)
J Neuropath Exp Neur
, vol.61
, pp. 368-374
-
-
Baes, M.1
Gressens, P.2
Huyghe, S.3
De Nys, K.4
Qi, C.5
Jia, Y.6
-
27
-
-
0002169455
-
Glycogen. Methods of enzymatic analysis
-
Bergmeyer HU, ed. Weinheim, Germany: Verlag Chemie
-
Keppler D, Decker K. Glycogen. Methods of enzymatic analysis. In: Bergmeyer HU, ed. Metabolites 1: Carbohydrates. Weinheim, Germany: Verlag Chemie, 1984:11-18.
-
(1984)
Metabolites 1: Carbohydrates
, pp. 11-18
-
-
Keppler, D.1
Decker, K.2
-
28
-
-
0032032380
-
Protein serine/threonine phosphatase inhibitors suppress phenobarbital-induced Cyp2b10 gene transcription in mouse primary hepatocytes
-
Honkakoski P, Negishi M. Protein serine/threonine phosphatase inhibitors suppress phenobarbital-induced Cyp2b10 gene transcription in mouse primary hepatocytes. Biochem J 1998;330:889-895.
-
(1998)
Biochem J
, vol.330
, pp. 889-895
-
-
Honkakoski, P.1
Negishi, M.2
-
29
-
-
0025806764
-
Intracellular heterogeneity in mitochondrial membrane potentials revealed by a J-aggregate-forming lipophilic cation JC-1
-
Smiley ST, Reers M, Mottola-Hartshorn C, Lin M, Chen A, Smith TW, et al. Intracellular heterogeneity in mitochondrial membrane potentials revealed by a J-aggregate-forming lipophilic cation JC-1. Proc Natl Acad Sci U S A 1991:88:3671-3675.
-
(1991)
Proc Natl Acad Sci U S A
, vol.88
, pp. 3671-3675
-
-
Smiley, S.T.1
Reers, M.2
Mottola-Hartshorn, C.3
Lin, M.4
Chen, A.5
Smith, T.W.6
-
30
-
-
0036024976
-
Measuring mitochondrial reactive oxygen species
-
Degli Esposti M, Measuring mitochondrial reactive oxygen species. Methods 2002;26:335-340.
-
(2002)
Methods
, vol.26
, pp. 335-340
-
-
Degli Esposti, M.1
-
31
-
-
0043166954
-
Decrease of intracellular ATP content downregulated UCP2 expression in mouse hepatocytes
-
Cheng G, Polito CC, Haines JK, Shafizadeh SF, Fiorini RN, Zhou X, et al. Decrease of intracellular ATP content downregulated UCP2 expression in mouse hepatocytes. Biochem Biophys Res Commun 2003;308:573-580.
-
(2003)
Biochem Biophys Res Commun
, vol.308
, pp. 573-580
-
-
Cheng, G.1
Polito, C.C.2
Haines, J.K.3
Shafizadeh, S.F.4
Fiorini, R.N.5
Zhou, X.6
-
32
-
-
0036310142
-
Mitochondrial dysfunction in a cell culture model of familial amyotrophic lateral sclerosis
-
Menzies FM, Cookson MR, Taylor RW, Turnbull DM, Chrzanowska-Lightowlers ZM, Dong L, et al. Mitochondrial dysfunction in a cell culture model of familial amyotrophic lateral sclerosis. Brain 2002;125:1522-1533.
-
(2002)
Brain
, vol.125
, pp. 1522-1533
-
-
Menzies, F.M.1
Cookson, M.R.2
Taylor, R.W.3
Turnbull, D.M.4
Chrzanowska- Lightowlers, Z.M.5
Dong, L.6
-
33
-
-
2442696086
-
Transcription coactivator PBP, the peroxisome proliferator-activated receptor (PPAR)-binding protein, is required for PPARα-regulated gene expression in liver
-
Jia Y, Qi C, Kashireddi P, Surapureddi S, Zhu Y-Z, Rao MS, et al. Transcription coactivator PBP, the peroxisome proliferator-activated receptor (PPAR)-binding protein, is required for PPARα-regulated gene expression in liver. J Biol Chem 2004;279:24427-24434.
-
(2004)
J Biol Chem
, vol.279
, pp. 24427-24434
-
-
Jia, Y.1
Qi, C.2
Kashireddi, P.3
Surapureddi, S.4
Zhu, Y.-Z.5
Rao, M.S.6
-
34
-
-
0032546929
-
Steatohepatitis, spontaneous peroxisome proliferation and liver tumors in mice lacking peroxisomal fatty acyl-CoA oxidase
-
Fan C-Y, Pan J, Usuda N, Yeldandi AV, Rao MS, Reddy JK. Steatohepatitis, spontaneous peroxisome proliferation and liver tumors in mice lacking peroxisomal fatty acyl-CoA oxidase. J Biol Chem 1998;273:15639-15645.
-
(1998)
J Biol Chem
, vol.273
, pp. 15639-15645
-
-
Fan, C.-Y.1
Pan, J.2
Usuda, N.3
Yeldandi, A.V.4
Rao, M.S.5
Reddy, J.K.6
-
35
-
-
10744224980
-
Overexpression of peroxisome proliferator-activated receptor-alpha (PPARalpha)-regulated genes in liver in the absence of peroxisome proliferation in mice deficient in both L- and D- forms of enoyl-CoA hydratase/dehydrogenase enzymes of peroxisomal beta-oxidation system
-
Jia Y, Qi C, Zhang Z, Hashimoto T, Rao MS, Huyghe S, et al. Overexpression of peroxisome proliferator-activated receptor-alpha (PPARalpha)-regulated genes in liver in the absence of peroxisome proliferation in mice deficient in both L- and D- forms of enoyl-CoA hydratase/dehydrogenase enzymes of peroxisomal beta-oxidation system. J Biol Chem 2003;278:47232-47239.
-
(2003)
J Biol Chem
, vol.278
, pp. 47232-47239
-
-
Jia, Y.1
Qi, C.2
Zhang, Z.3
Hashimoto, T.4
Rao, M.S.5
Huyghe, S.6
-
36
-
-
0346993671
-
Disturbed cholesterol homeostasis in a peroxisome-deficient PEX2 knockout mouse model
-
Kovacs WJ, Shackelford JE, Tape KN, Richards MJ, Faust PL, Fliesler SJ, et al. Disturbed cholesterol homeostasis in a peroxisome-deficient PEX2 knockout mouse model. Mol Cell Biol 2004;24:1-13.
-
(2004)
Mol Cell Biol
, vol.24
, pp. 1-13
-
-
Kovacs, W.J.1
Shackelford, J.E.2
Tape, K.N.3
Richards, M.J.4
Faust, P.L.5
Fliesler, S.J.6
-
37
-
-
0042632799
-
Pex13 inactivation in the mouse disrupts peroxisome biogenesis and leads to a Zellweger syndrome phenotype
-
Maxwell M, Bjorkman J, Nguyen T, Sharp P, Finnie J, Paterson C, et al. Pex13 inactivation in the mouse disrupts peroxisome biogenesis and leads to a Zellweger syndrome phenotype. Mol Cell Biol 2003;23:5947-5957.
-
(2003)
Mol Cell Biol
, vol.23
, pp. 5947-5957
-
-
Maxwell, M.1
Bjorkman, J.2
Nguyen, T.3
Sharp, P.4
Finnie, J.5
Paterson, C.6
-
38
-
-
0842345390
-
Subcellular heterogeneity of mitochondrial function and dysfunction: Evidence obtained by confocal imaging
-
Kuznetsov AV, Usson Y, Leverve XMR. Subcellular heterogeneity of mitochondrial function and dysfunction: evidence obtained by confocal imaging. Mol Cell Biochem 2004;256:359-365.
-
(2004)
Mol Cell Biochem
, vol.256
, pp. 359-365
-
-
Kuznetsov, A.V.1
Usson, Y.2
Leverve, X.M.R.3
-
39
-
-
0031713986
-
Disorders of the mitochondria
-
Treem WR, Sokol RJ. Disorders of the mitochondria. Semin Liver Dis 1998;18:237-253.
-
(1998)
Semin Liver Dis
, vol.18
, pp. 237-253
-
-
Treem, W.R.1
Sokol, R.J.2
-
40
-
-
0030615104
-
Dependence of H2O2 formation by rat heart mitochondria on substrate availability and donor age
-
Hansford RG, Hogue BA, Mildaziene V. Dependence of H2O2 formation by rat heart mitochondria on substrate availability and donor age. J Bioenerg Biomembr 1997;29:89-95.
-
(1997)
J Bioenerg Biomembr
, vol.29
, pp. 89-95
-
-
Hansford, R.G.1
Hogue, B.A.2
Mildaziene, V.3
-
41
-
-
0033522924
-
Titrating the effects of mitochondrial complex I impairment in the cell physiology
-
Barrientos A, Moraes CT. Titrating the effects of mitochondrial complex I impairment in the cell physiology. J Biol Chem 1999;274:16188-16197.
-
(1999)
J Biol Chem
, vol.274
, pp. 16188-16197
-
-
Barrientos, A.1
Moraes, C.T.2
-
42
-
-
0030056515
-
Mitochondrial complex I deficiency leads to increased production of superoxide radicals and induction of superoxide dismutase
-
Pitkänen S, Robinson BH. Mitochondrial complex I deficiency leads to increased production of superoxide radicals and induction of superoxide dismutase. J Clin Invest 1996:98:345-351.
-
(1996)
J Clin Invest
, vol.98
, pp. 345-351
-
-
Pitkänen, S.1
Robinson, B.H.2
-
43
-
-
0346059551
-
Decrease in mitochondrial complex I activity in ischemic/reperfused rat heart
-
Paradies G, Petrosillo G, Pistolese M, Di Venosa N, Federici A, Ruggiero FR. Decrease in mitochondrial complex I activity in ischemic/reperfused rat heart. Circ Res 2004;94:53-59.
-
(2004)
Circ Res
, vol.94
, pp. 53-59
-
-
Paradies, G.1
Petrosillo, G.2
Pistolese, M.3
Di Venosa, N.4
Federici, A.5
Ruggiero, F.R.6
-
44
-
-
0042389608
-
Evidence for increased oxidative stress in peroxisomal D-bifunctional protein deficiency
-
Ferdinandusse S, Finckh B, de Hingh YC, Stroomer LE, Denis S, Kohlschutter A, et al. Evidence for increased oxidative stress in peroxisomal D-bifunctional protein deficiency. Mol Genet Metab 2003;79:281-287.
-
(2003)
Mol Genet Metab
, vol.79
, pp. 281-287
-
-
Ferdinandusse, S.1
Finckh, B.2
De Hingh, Y.C.3
Stroomer, L.E.4
Denis, S.5
Kohlschutter, A.6
-
45
-
-
0026654982
-
Reduced activity of the electron transport chain in liver mitochondria isolated from rats with secondary biliary cirrhosis
-
Krähenbühl S, Stucki J, Reichen J. Reduced activity of the electron transport chain in liver mitochondria isolated from rats with secondary biliary cirrhosis. HEPATOLOGY 1992;15:1160-1166.
-
(1992)
Hepatology
, vol.15
, pp. 1160-1166
-
-
Krähenbühl, S.1
Stucki, J.2
Reichen, J.3
-
46
-
-
0028091169
-
Toxicity of bile acids on the electron transport chain of isolated rat liver mitochondria
-
Krähenbühl S, Talos C, Fischer S, Reichen J. Toxicity of bile acids on the electron transport chain of isolated rat liver mitochondria. HEPATOLOGY 1994;19:471-479.
-
(1994)
Hepatology
, vol.19
, pp. 471-479
-
-
Krähenbühl, S.1
Talos, C.2
Fischer, S.3
Reichen, J.4
-
47
-
-
0037219061
-
Role of ALDP (ABCD1) and mitochondria in X-linked adrenoleukodystrophy
-
McGuinness MC, Lu J-F, Zhang H-P, Dong G-X, Heinzer AK, Watkins PA, et al. Role of ALDP (ABCD1) and mitochondria in X-linked adrenoleukodystrophy. Mol Cell Biol 2003:23:744-753.
-
(2003)
Mol Cell Biol
, vol.23
, pp. 744-753
-
-
McGuinness, M.C.1
Lu, J.-F.2
Zhang, H.-P.3
Dong, G.-X.4
Heinzer, A.K.5
Watkins, P.A.6
-
48
-
-
0033057924
-
The effect of peroxisome proliferators on mitochondrial bioenergetics
-
Zhou S, Wallace KB. The effect of peroxisome proliferators on mitochondrial bioenergetics. Toxicol Sci 1999:48:82-89.
-
(1999)
Toxicol Sci
, vol.48
, pp. 82-89
-
-
Zhou, S.1
Wallace, K.B.2
-
49
-
-
2942592344
-
Mitochondrial respiratory chain dysfunction, a non-receptor-mediated effect of synthetic PPAR-ligands: Biochemical and pharmacological implications
-
Scatena R, Bottoni P, Martorana GE, Ferrari F, De Sole P, Rossi C, et al. Mitochondrial respiratory chain dysfunction, a non-receptor-mediated effect of synthetic PPAR-ligands: biochemical and pharmacological implications. Biochem Biophys Res Commun 2004:319:967-973.
-
(2004)
Biochem Biophys Res Commun
, vol.319
, pp. 967-973
-
-
Scatena, R.1
Bottoni, P.2
Martorana, G.E.3
Ferrari, F.4
De Sole, P.5
Rossi, C.6
-
50
-
-
0033613869
-
Phytanic acid activates the peroxisome proliferator-activated receptor α (PPARα) in sterol carrier protein 2-/sterol carrier protein x-deficient mice
-
Ellinghaus P, Wolfrum C, Assmann G, Spener F, Seedorf U. Phytanic acid activates the peroxisome proliferator-activated receptor α (PPARα) in sterol carrier protein 2-/sterol carrier protein x-deficient mice. J Biol Chem 1999;274:2766-2772.
-
(1999)
J Biol Chem
, vol.274
, pp. 2766-2772
-
-
Ellinghaus, P.1
Wolfrum, C.2
Assmann, G.3
Spener, F.4
Seedorf, U.5
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