Pathogenesis of human mitochondrial diseases is modulated by reduced activity of the ubiquitin/proteasome system

Cell Metabolism

Volumn 19, Issue 4, 2014, Pages 642-652

  Segref, Alexandra ^a   Kevei, Éva ^a   Pokrzywa, Wojciech ^a   Schmeisser, Kathrin ^b   Mansfeld, Johannes ^b,e   Livnat Levanon, Nurit ^c   Ensenauer, Regina ^d   Glickman, Michael H ^c   Ristow, Michael ^b,e   Hoppe, Thorsten ^a  

^a UNIVERSITY OF COLOGNE   (Germany)

^b FRIEDRICH SCHILLER UNIVERSITY JENA   (Germany)

^c TECHNION ISRAEL INSTITUTE OF TECHNOLOGY   (Israel)

^d LUDWIG MAXIMILIANS UNIVERSITY   (Germany)

^e ETH ZURICH   (Switzerland)

Author keywords

[No Author keywords available]

Indexed keywords

CYCLOOXYGENASE 1; ISOVALERYL COENZYME A DEHYDROGENASE; PROTEASOME; REACTIVE OXYGEN METABOLITE; UBIQUITIN; ADENOSINE TRIPHOSPHATE; GREEN FLUORESCENT PROTEIN; MITOTRACKER RED 580; ORGANIC COMPOUND; PTGS1 PROTEIN, HUMAN; UBIQUITIN PROTEIN LIGASE;

ARTICLE; BREATHING; CAENORHABDITIS ELEGANS; CELL STRESS; DISEASE COURSE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; HUMAN; HUMAN CELL; MITOCHONDRIAL RESPIRATION; NONHUMAN; OXIDATIVE STRESS; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN HOMEOSTASIS; WORM; ANIMAL; CELL LINE; GENETICS; IMMUNOBLOTTING; METABOLISM; MUTAGENESIS; OXIDATIVE PHOSPHORYLATION; PATHOPHYSIOLOGY; POLYACRYLAMIDE GEL ELECTROPHORESIS; TRANSGENIC ANIMAL;

ADENOSINE TRIPHOSPHATE; ANIMALS; ANIMALS, GENETICALLY MODIFIED; CAENORHABDITIS ELEGANS; CELL LINE; CYCLOOXYGENASE 1; ELECTROPHORESIS, POLYACRYLAMIDE GEL; GREEN FLUORESCENT PROTEINS; HUMANS; IMMUNOBLOTTING; MITOCHONDRIAL DISEASES; MUTAGENESIS; ORGANIC CHEMICALS; OXIDATIVE PHOSPHORYLATION; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEOLYSIS; REACTIVE OXYGEN SPECIES; UBIQUITIN; UBIQUITIN-PROTEIN LIGASES;

EID: 84897528338     PISSN: 15504131     EISSN: 19327420     Source Type: Journal    
DOI: 10.1016/j.cmet.2014.01.016     Document Type: Article

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