Mitochondrial dysfunction and oxidative damage cooperatively fuel axonal degeneration in X-linked adrenoleukodystrophy

Biochimie

Volumn 98, Issue 1, 2014, Pages 143-149

  Fourcade, Stéphane ^a,b   López Erauskin, Jone ^a,b   Ruiz, Montserrat ^a,b   Ferrer, Isidre ^a,c   Pujol, Aurora ^a,b,d  

^a HOSPITAL UNIVERSITARI DE BELLVITGE   (Spain)

^b CENTRO DE INVESTIGACIÓN BIOMÉDICA EN RED DE ENFERMEDADES RARAS CIBERER   (Spain)

^c CENTRO DE INVESTIGACIÓN BIOMÉDICA EN RED SOBRE ENFERMEDADES NEURODEGENERATIVAS CIBERNED   (Spain)

^d INSTITUCIÓ CATALANA DE RECERCA I ESTUDIS AVANÇATS ICREA   (Spain)

Author keywords

Cyclophilin D; Mitochondria dysfunction; Oxidative damage; Proteasome; Very long chain fatty acids; X linked adrenoleukodystrophy

Indexed keywords

MITOCHONDRIAL PROTEIN; PIOGLITAZONE; PROTEASOME; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE;

ADRENOLEUKODYSTROPHY; ALZHEIMER DISEASE; AMYOTROPHIC LATERAL SCLEROSIS; BIOENERGY; BIOGENESIS; CELL DISRUPTION; CHILDHOOD ADRENOLEUKODYSTROPHY; DISEASE COURSE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FIBROBLAST; HUNTINGTON CHOREA; METABOLIC SYNDROME X; MITOCHONDRION; MULTIPLE SCLEROSIS; NERVE FIBER DEGENERATION; NONHUMAN; OXIDATIVE STRESS; PARKINSON DISEASE; PATHOGENESIS; PHENOTYPE; PROTEIN EXPRESSION; REVIEW;

CYCLOPHILIN D; MITOCHONDRIA DYSFUNCTION; OXIDATIVE DAMAGE; PROTEASOME; VERY LONG-CHAIN FATTY ACIDS; X-LINKED ADRENOLEUKODYSTROPHY;

ADRENOLEUKODYSTROPHY; ANIMALS; ATP-BINDING CASSETTE TRANSPORTERS; AXONS; DISEASE MODELS, ANIMAL; ENERGY METABOLISM; FATTY ACIDS; MICE; MICE, KNOCKOUT; MITOCHONDRIA; NEURODEGENERATIVE DISEASES; OXIDATIVE STRESS; PROTEASOME ENDOPEPTIDASE COMPLEX;

EID: 84895106927     PISSN: 03009084     EISSN: 61831638     Source Type: Journal    
DOI: 10.1016/j.biochi.2013.09.012     Document Type: Short Survey

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