Early oxidative damage underlying neurodegeneration in X-adrenoleukodystrophy

Human Molecular Genetics

Volumn 17, Issue 12, 2008, Pages 1762-1773

  Fourcade, Stéphane ^a,b,c   López Erauskin, Jone ^a,b,c   Galino, Jorge ^a,b,c   Duval, Carine ^a,b,c   Naudi, Alba ^d   Jove, Mariona ^d   Kemp, Stephan ^e,f   Villarroya, Francesc ^c,g   Ferrer, Isidre ^c,h   Pamplona, Reinald ^d   Portero Otin, Manuel ^d   Pujol, Aurora ^a,b,c,i  

^a HOSPITAL UNIVERSITARI DE BELLVITGE   (Spain)

^b CENTRO DE INVESTIGACIÓN BIOMÉDICA EN RED DE ENFERMEDADES RARAS CIBERER   (Spain)

^c UNIVERSITY OF BARCELONA   (Spain)

^d UNIVERSITY OF LLEIDA   (Spain)

^e Department of Clinical Chemistry ^*

^f UNIVERSITY OF AMSTERDAM   (Netherlands)

^g INSTITUTO DE SALUD CARLOS III   (Spain)

^h CENTRO DE INVESTIGACIÓN BIOMÉDICA EN RED SOBRE ENFERMEDADES NEURODEGENERATIVAS CIBERNED   (Spain)

ⁱ INSTITUCIÓ CATALANA DE RECERCA I ESTUDIS AVANÇATS ICREA   (Spain)

Author keywords

[No Author keywords available]

Indexed keywords

ABC TRANSPORTER; ALPHA TOCOPHEROL DERIVATIVE; LYSINE; MALONALDEHYDE; PROTEIN ABCD1; TROLOX C; VERY LONG CHAIN FATTY ACID;

ADRENOLEUKODYSTROPHY; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ANTIOXIDANT ACTIVITY; ARTICLE; CONTROLLED STUDY; DRUG RESPONSE; ENZYME ACTIVITY; EX VIVO STUDY; FIBROBLAST; GENE FUNCTION; GENE LOSS; GLUCOSE OXIDATION; HUMAN; HUMAN CELL; IN VITRO STUDY; KNOCKOUT MOUSE; LIPID OXIDATION; LIPID STORAGE; MASS FRAGMENTOGRAPHY; METAL METABOLISM; MOUSE; NERVE DEGENERATION; NERVOUS TISSUE; NEUROPATHOLOGY; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; PROTEIN METABOLISM; SPINAL CORD; TISSUE DISTRIBUTION; TISSUE LEVEL; X CHROMOSOME LINKED DISORDER;

ADRENOLEUKODYSTROPHY; ANIMALS; CATALASE; CHEMOKINE CCL22; CHROMANS; FATTY ACIDS; FIBROBLASTS; HUMANS; LYSINE; MALONDIALDEHYDE; MEMBRANE POTENTIAL, MITOCHONDRIAL; MICE; MICE, INBRED C57BL; MOTOR NEURONS; OXIDATION-REDUCTION; OXIDATIVE STRESS; SPINAL CORD; SUPEROXIDE DISMUTASE;

MUS;

EID: 44849100253     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddn085     Document Type: Article

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