Mitochondrial dysfunction in ALS

Progress in Neurobiology

Volumn 97, Issue 2, 2012, Pages 54-66

  Cozzolino, Mauro ^a   Carrì, Maria Teresa ^a,b  

^a IRCCS FONDAZIONE SANTA LUCIA   (Italy)

^b UNIVERSITY OF ROME TOR VERGATA   (Italy)

Author keywords

Amyotrophic lateral sclerosis; Mitochondria; Motor neuron; SOD1

Indexed keywords

ADENOSINE TRIPHOSPHATE; BH3 PROTEIN; CALCIUM ION; COPPER ZINC SUPEROXIDE DISMUTASE; CYTOCHROME C OXIDASE; GLUTAMIC ACID; MANGANESE SUPEROXIDE DISMUTASE; MICROTUBULE ASSOCIATED PROTEIN 1; MITOCHONDRIAL DNA; MITOCHONDRIAL PROTEIN; PROTEIN BAX; PROTEIN BCL 2; REACTIVE OXYGEN METABOLITE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); VOLTAGE DEPENDENT ANION CHANNEL 1; X LINKED INHIBITOR OF APOPTOSIS;

AMYOTROPHIC LATERAL SCLEROSIS; APOPTOSIS; ASTROCYTE; BRAIN CORTEX; BRAIN STEM; CALCIUM HOMEOSTASIS; CELL DEATH; CELL MEMBRANE; CYTOSOL; DNA DAMAGE; ENERGY YIELD; EXCITOTOXICITY; FAMILIAL DISEASE; FRONTAL CORTEX; HUMAN; IMMUNOREACTIVITY; META ANALYSIS (TOPIC); MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL RESPIRATION; MITOCHONDRION; MORPHOLOGY; MOTONEURON; MULTICENTER STUDY (TOPIC); NERVE ENDING; NERVE FIBER TRANSPORT; NEUROMUSCULAR SYNAPSE; NONHUMAN; OXIDATIVE PHOSPHORYLATION; OXIDATIVE STRESS; PHASE 2 CLINICAL TRIAL (TOPIC); PHASE 3 CLINICAL TRIAL (TOPIC); PRIORITY JOURNAL; PROTEIN LOCALIZATION; PYRAMIDAL NERVE CELL; RANDOMIZED CONTROLLED TRIAL (TOPIC); RESPIRATORY CHAIN; REVIEW; SPINAL CORD;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CALCIUM; HUMANS; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MOTOR NEURONS; OXIDATIVE STRESS; SUPEROXIDE DISMUTASE;

EID: 84860650335     PISSN: 03010082     EISSN: 18735118     Source Type: Journal    
DOI: 10.1016/j.pneurobio.2011.06.003     Document Type: Review

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