Toxicity of familial ALS-linked SOD1 mutants from selective recruitment to spinal mitochondria

Neuron

Volumn 43, Issue 1, 2004, Pages 5-17

  Liu, Jian ^a   Lillo, Concepción ^b   Jonsson, P Andreas ^c   Velde, Christine Vande ^a   Ward, Christopher M ^a   Miller, Timothy M ^a   Subramaniam, Jamuna R ^e   Rothstein, Jeffery D ^e   Marklund, Stefan ^c   Andersen, Peter M ^d   Brännström, Thomas ^c   Gredal, Ole ^f   Wong, Philip C ^e   Williams, David S ^b   Cleveland, Don W ^a  

^a LUDWIG INSTITUTE FOR CANCER RESEARCH   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c UMEÅ UNIVERSITY   (Sweden)

^d UMEÅ UNIVERSITY HOSPITAL   (Sweden)

^e JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^f BISPEBJERG HOSPITAL   (Denmark)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; COVALENT BOND; CROSS LINKING; CYTOPLASM; ENZYME ACTIVATION; GENE MUTATION; GENETIC LINKAGE; HUMAN; HUMAN CELL; HUMAN TISSUE; MITOCHONDRION; MOUSE; NEUROTOXICITY; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; RAT; SPINAL CORD;

AGING; ANIMALS; CYTOPLASM; DISEASE MODELS, ANIMAL; HUMANS; INTRACELLULAR MEMBRANES; MACROMOLECULAR SUBSTANCES; MICE; MICE, TRANSGENIC; MICROSCOPY, ELECTRON; MITOCHONDRIA; MITOCHONDRIAL PROTEINS; MOLECULAR CHAPERONES; MOTOR NEURON DISEASE; MUTATION; NERVE DEGENERATION; PROTEIN BINDING; PROTEIN FOLDING; PROTEIN ISOFORMS; PROTEIN TRANSPORT; SPINAL CORD; SUPEROXIDE DISMUTASE;

EID: 3242701496     PISSN: 08966273     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.neuron.2004.06.016     Document Type: Article

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