Mitochondrial dysfunction due to mutant copper/zinc superoxide dismutase associated with amyotrophic lateral sclerosis is reversed by N-acetylcysteine

Neurobiology of Disease

Volumn 13, Issue 3, 2003, Pages 213-221

  Beretta, Simone ^a   Sala, Gessica ^a   Mattavelli, Laura ^a   Ceresa, Chiara ^a   Casciati, Arianna ^b   Ferri, Alberto ^b,c   Carrì, Maria Teresa ^b,d   Ferrarese, Carlo ^a  

^a SAN GERARDO HOSPITAL   (Italy)

^b Ctro Neurbio Sperim Mondino T   (Italy)

^c CNR Consiglio Nazionale delle Ricerche   (Italy)

^d UNIVERSITY OF ROME TOR VERGATA   (Italy)

Author keywords

Amyotrophic lateral sclerosis; Mitochondrial function; N Acetylcysteine; Oxidative stress; SOD1

Indexed keywords

3 (4,5 DIMETHYL 2 THIAZOLYL) 2,5 DIPHENYLTETRAZOLIUM; ACETYLCYSTEINE; ADENOSINE TRIPHOSPHATE; COPPER ZINC SUPEROXIDE DISMUTASE; REACTIVE OXYGEN METABOLITE; TETRAZOLIUM; UNCLASSIFIED DRUG;

AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; CANCER CELL CULTURE; CELL DEATH; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; GENE EXPRESSION; GENE OVEREXPRESSION; HOMEOSTASIS; HUMAN; HUMAN CELL; NEUROBLASTOMA CELL; PRIORITY JOURNAL; REDUCTION; WILD TYPE;

EID: 0042093555     PISSN: 09699961     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0969-9961(03)00043-3     Document Type: Article

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